Echogenic Splenic Lesions in a Child with Type B Niemann-Pick Disease

被引:3
作者
Adin, Mehmet Emin [1 ]
Onder, Hakan [1 ]
Alabalik, Ulas [2 ]
机构
[1] Dicle Univ, Sch Med, Dept Radiol, TR-21280 Diyarbakir, Turkey
[2] Dicle Univ, Sch Med, Dept Pathol, TR-21280 Diyarbakir, Turkey
关键词
Niemann-Pick disease; spleen; ultrasound; color Doppler ultrasonography; FEATURES;
D O I
10.1002/jcu.22009
中图分类号
O42 [声学];
学科分类号
070206 ; 082403 ;
摘要
We report the case of a 15-year-old boy with Niemann-Pick disease type B with characteristic sonographic findings of splenic involvement. There were multiple well-defined echogenic nodular lesions within the spleen parenchyma, and these lesions were surrounded by ring-like blood flow on color Doppler imaging. Most of the patients with Niemann-Pick disease type B are children and they undergo repeated imaging studies. Therefore, familiarity with sonographic findings of the disease is required. (c) 2012 Wiley Periodicals, Inc. J Clin Ultrasound41:32-34, 2013
引用
收藏
页码:32 / 34
页数:3
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