Congenital multiple cavernous angiomas associated with thrombosed arteriovenous malformation of the brain - Case report

被引:3
作者
Hayashi, Y [1 ]
Tohma, Y [1 ]
Mouri, M [1 ]
Yamashima, T [1 ]
Yamashita, J [1 ]
机构
[1] Kanazawa Univ, Sch Med, Dept Neurosurg, Kanazawa, Ishikawa 9208641, Japan
关键词
multiple vascular malformations; cavernous angioma; thrombosed arteriovenous malformation; familial occurrence;
D O I
10.2176/nmc.42.67
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 16-year-old girl presented with multiple cerebral cavernous angiomas with calcifications due to repeated hemorrhages and a thrombosed cerebral arteriovenous malformation (AVM). Her 18-year-old elder sister also had multiple cerebral cavernous angiomas associated with calcifications, which suggested presence of repeated previous hemorrhages. Surgical removal via a right occipital craniotomy resulted in a good outcome. The histological diagnosis was thrombosed AVM. Evaluation of congenital vascular anomaly needs to take into consideration the combination of other congenital vascular anomalies and their familial occurrence.
引用
收藏
页码:67 / 72
页数:6
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