Laryngeal stenosis in a patient with severe congenital neutropenia

被引：0

作者：

Bando, Hideki ^{[1
]}

Nagao, Hikaru ^{[1
]}

Nishio, Takeshi ^{[1
]}

Hirota, Ryuichi ^{[1
]}

Sakaguchi, Hirofumi ^{[1
]}

Imamura, Toshihiko ^{[2
]}

Hisa, Yasuo ^{[1
]}

机构：

[1] Kyoto Prefectural Univ Med, Dept Otolaryngol Head & Neck Surg, Kyoto 6028566, Japan

[2] Kyoto Prefectural Univ Med, Dept Pediat, Kyoto 6028566, Japan

来源：

LARYNGOSCOPE | 2013年 / 123卷 / 02期

关键词：

Larynx; stenosis; Kostmann; severe congenital neutropenia;

D O I：

10.1002/lary.23375

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

Objectives/Hypothesis: We report the first case of laryngeal stenosis with granuloma in a patient with severe congenital neutropenia (SCN). Study Design: Case report and retrospective review. Methods: Review of medical records. Results: A 6-year-old female who was diagnosed with SCN presented with a cough and wheezing. An endoscopic study revealed laryngeal stenosis with granuloma. Tracheotomy and direct laryngoscopy were performed under general anesthesia, and administration of granulocyte colony-stimulating factor was started. The laryngeal granuloma disappeared 3 weeks later, and the tracheal stoma was closed. Conclusions: Presence of a laryngeal lesion should be considered in SCN patients with persistent airway symptoms.

引用

页码：455 / 457

页数：3

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