Fibrosing organising pneumonia

被引:43
作者
Beardsley, Brooke [1 ]
Rassl, Doris [2 ]
机构
[1] Canterbury Hlth Labs, Dept Anat Pathol, Christchurch, New Zealand
[2] Papworth Hosp, Dept Histopathol, Cambridge CB23 3RE, England
关键词
Lung; Inflammation; fibrosis; IDIOPATHIC BRONCHIOLITIS OBLITERANS; INTRALUMINAL FIBROMYXOID LESIONS; INTERSTITIAL LUNG-DISEASE; CLINICAL-FEATURES; PULMONARY-FIBROSIS; CONNECTIVE-TISSUE; CT FINDINGS; BOOP; SECONDARY; DERMATOMYOSITIS;
D O I
10.1136/jclinpath-2012-201342
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Organising pneumonia (otherwise referred to as bronchiolitis obliterans organising pneumonia) is characterised histologically by plugs of granulation tissue, which are present predominantly within small airways, alveolar ducts and peri-bronchiolar alveoli. This pattern is not specific for any disorder or cause, but is one type of inflammatory response to pulmonary injury, which may be seen in a wide variety of clinical conditions. Typically, organising pneumonia responds very well to corticosteroid treatment; however, a small percentage of patients appear to develop progressive fibrosis.
引用
收藏
页码:875 / 881
页数:7
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