Acromegaly due to pituitary macroadenoma in a patient with McCune-Albright syndrome. Case report and literature overview

被引：0

作者：

Concepcion-Zavaleta, Marcio ^{[1
]}

Ramos-Yataco, Anthony ^{[2
]}

Rios-Rojas, Jeniffer ^{[3
]}

Concepcion-Urteaga, Luis ^{[4
]}

Alcalde-Loyola, Carlos ^{[4
]}

Ildefonso-Najarro, Sofia ^{[5
]}

Gallardo-Rojas, Wilson ^{[5
]}

机构：

[1] Clin Stella Maris, Serv Endocrinol, Lima, Peru

[2] Hosp Ricardo Cruzado Rivarola, Serv Med Interna, Ica, Peru

[3] Univ Nacl Mayor San Marcos, Escuela Med, Lima, Peru

[4] Univ Nacl Trujillo Trujillo, Escuela Med, Trujillo, Peru

[5] Hosp Nacl Guillermo Almenera Irigoyen, EsSalud, Serv Endocrinol, Lima, Peru

来源：

REVISTA DEL CUERPO MEDICO DEL HOSPITAL NACIONAL ALMANZOR AGUINAGA ASENJO | 2022年 / 15卷 / 02期

关键词：

Acromegaly; Growth Hormone-Secreting Pituitary Adenoma; Fibrous Dysplasia; Polyostotic;

D O I：

暂无

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Background: McCune-Albright syndrome (MAS) is a rare disease characterized by the triad: cafe-au-lait skin spots, polyostotic fibrous dysplasia, and precocious puberty. It can affect various hormonal axes, including growth hormone (GH), and may be associated with acromegaly. Case report: We describe the case of a 44-year-old woman with peripheral precocious puberty, abnormal uterine bleeding, growth of the hands and feet, prognathism, frontal prominence, cafe-au-lait spots, and stony tumors on the face and forearms. Results: Supported by laboratory and imaging tests, the diagnoses of acromegaly, hypogonadotropic hypogonadism and McCune-Albright syndrome were reached. The patient underwent surgical treatment with persistence of clinical and laboratory disease. Conclusion: Timely diagnosis and treatment of acromegaly and its complications will provide a better prognosis for patients with MAS

引用

页码：273 / 276

页数：4

共 17 条

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