Steroid-Refractory Protein-Losing Enteropathy with Gastrointestinal Bleeding in a Patient with Fontan Circulation A Case Report and Literature Review

被引：0
作者：
Iwamoto, Yoichi [1 ]
Matsumura, Shun [1 ]
Ishido, Hirotaka [1 ]
Senzaki, Hideaki [2 ]
Masutani, Satoshi [1 ]
机构：
[1] Saitama Med Univ, Dept Pediat, Saitama Med Ctr, 1981 Kamoda, Kawagoe, Saitama 3508550, Japan
[2] Int Univ Hlth & Welf Narita Hosp, Dept Pediat, Chiba, Japan
来源：
INTERNATIONAL HEART JOURNAL | 2020年 / 61卷 / 04期
关键词：
Hypoalbuminemia; Anemia; Hypoplastic left heart syndrome; Total cavopulmonary connection; Steroid; HEMORRHAGE;
D O I：
10.1536/ihj.20-038
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Protein-losing enteropathy (PLE) is one of the major complications after a Fontan operation. Some PLE patients suffer from concurrent gastrointestinal bleeding. An effective treatment regimen for such patients has not been established yet. Further, it remains unknown whether PLE and gastrointestinal bleeding coexist inde-pendently, or protein losing is associated with gastrointestinal bleeding. We report a 7-year-old steroid-refractory post-Fontan PLE case suggesting the latter pathogenesis together with a literature review.
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收藏
页码：851 / 855
页数：5
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