Tetralogy of Fallot With Absent Pulmonary Valve and Nonconfluent Pulmonary Arteries: A Management Conundrum

被引：2

作者：

Swaminathan, Sethuraman ^{[1
]}

Agarwal, Arpit ^{[1
]}

Infante, Juan C. ^{[2
]}

Rosenkranz, Eliot ^{[3
]}

机构：

[1] Univ Miami, Miller Sch Med, Jackson Mem Med Ctr, Div Pediat Cardiol,Dept Pediat,Holtz Childrens Ho, 1611 NW 12 Ave,North Wing,Room 109, Miami, FL 33136 USA

[2] Univ Miami, Miller Sch Med, Jackson Mem Med Ctr, Dept Radiol,Holtz Childrens Hosp, Miami, FL 33136 USA

[3] Univ Miami, Miller Sch Med, Jackson Mem Med Ctr,Holtz Childrens Hosp, Div Pediat Cardiothorac Surg,Dept Surg, Miami, FL 33136 USA

来源：

WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY | 2020年 / 11卷 / 04期

关键词：

tetralogy of Fallot; absent pulmonary valve syndrome; patent ductus arteriosus; nonconfluent pulmonary arteries; DUCTUS-ARTERIOSUS;

D O I：

10.1177/2150135118775661

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Tetralogy of Fallot with absent pulmonary valve syndrome is a rare form of congenital heart disease. Among the different variations with this rare anomaly is nonconfluent pulmonary artery branches with anomalous origin of the left pulmonary artery from the ductus arteriosus. The authors present one such case which was diagnosed prenatally to have tetralogy of Fallot with absent pulmonary valve and identified postnatally to have nonconfluent pulmonary artery branches in addition. We discuss the conundrum of respiratory management in this patient pre- and postoperatively due to a unique ventilation perfusion mismatch problem, which varies between the two lungs.

引用

页码：NP168 / NP171

页数：4

共 10 条

[1] Autologous Right Pulmonary Artery Tissue for Repair of Left Pulmonary Artery Originating from Left Patent Ductus Arteriosus in a Patient With Tetralogy of Fallot and Absent Pulmonary Valve [J].