Fatal Henoch-Schonlein Purpura in an Adult With Dieulafoy Lesions

被引：4

作者：

Cristescu, Dan A. ^{[1
]}

Yuvienco, Candice ^{[2
]}

Schwartz, Stuart ^{[2
]}

机构：

[1] Boston Univ, Div Rheumatol, Roger Williams Med Ctr, Boston, MA 02215 USA

[2] Brown Univ, Rhode Isl Hosp, Div Rheumatol, Providence, RI 02903 USA

来源：

JCR-JOURNAL OF CLINICAL RHEUMATOLOGY | 2012年 / 18卷 / 05期

关键词：

Henoch-Schonlein purpura; vasculitis; Dieulafoy lesion; gastrointestinal hemorrhage; adult; NEPHRITIS; CHILDHOOD; CYCLOPHOSPHAMIDE; PLASMAPHERESIS; CHILDREN; DISEASE;

D O I：

10.1097/RHU.0b013e318262e3f9

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Henoch-Schonlein purpura (HSP) is considered a benign disease of children. We report a severe case of HSP in an adult causing renal failure and gastrointestinal (GI) hemorrhage. Despite aggressive treatment with corticosteroids, cyclophosphamide, and plasmapheresis, the patient developed massive GI bleeding from 2 Dieulafoy lesions and died weeks after bowel resection. Although uncommon, when massive GI hemorrhage occurs, actively bleeding Dieulafoy lesions, although uncommon, should be suspected and evaluated early.

引用

页码：253 / 256

页数：4

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