Anorectal Malformations

被引:0
作者
Cretolle, C. [1 ]
Rousseau, V. [1 ]
Lottmann, H. [1 ]
Irtan, S. [1 ]
Lortat-Jacob, S. [1 ]
Alova, I. [1 ]
Michel, J. L. [2 ]
Aigrain, Y. [1 ]
Podevin, G. [3 ]
Lehur, R. A. [4 ]
Sarnacki, S. [1 ]
机构
[1] Univ Paris 05, Hop Necker Enfants Malad, CRMR Malformat Anorectales & Pelviennes Rares MAR, Serv Chirurg Pediat, F-75075 Paris, France
[2] Ctr Hosp Univ Felix Guyon, Serv Chirurg Pediat, F-97405 St Denis, France
[3] Hop Univ Angers, Serv Chirurg Pediat, F-49700 Angers, France
[4] Hop Univ Nantes, Inst Malad Appareil Digest, Clin Chirurg Digest & Endocrinienne, Hotel Dieu, F-44093 Nantes, France
来源
ARCHIVES DE PEDIATRIE | 2013年 / 20卷
关键词
POSTERIOR SAGITTAL ANORECTOPLASTY; HIGH IMPERFORATE ANUS; QUALITY-OF-LIFE; CURRARINO-SYNDROME; SPINAL DYSRAPHISM; CHILDREN; ANOMALIES; MANAGEMENT; DIAGNOSIS; RISK;
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Anorectal malformations (ARM) are the result of an abnormal development of the terminal part of the digestive tract interesting anus and/or rectum that occur early between the sixth and tenth week of embryonic development. They carry a malformation spectrum of severity depending on the level of disruption of the anorectal canal and of the associated caudal malformations (sacrum and spine). ARM are associated in over half the cases with other malformations that can be integrated in some cases in known syndromes. If surgical treatment to restore anatomy as normal as possible is indispensable, post-operative care is essential for these patients whose defecation mechanisms are altered, to reach if not continence, at least a socially acceptable cleanliness. (c) 2013 Elsevier Masson SAS. All rights reserved.
引用
收藏
页码:S19 / S27
页数:9
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