Ovarian adrenal rest tissue in congenital adrenal hyperplasia - A patient report

被引:0
|
作者
Claahsen-van der Grinten, HL
Hulsbergen-van de Kaa, CA
Otten, BJ
机构
[1] Radboud Univ Nijmegen Med Ctr, Dept Metab & Endocrine Dis, NL-6500 HB Nijmegen, Netherlands
[2] Radboud Univ Nijmegen Med Ctr, Dept Pathol, NL-6500 HB Nijmegen, Netherlands
来源
JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM | 2006年 / 19卷 / 02期
关键词
congenital adrenal hyperplasia; ovarian adrenal rest; testicular adrenal rest tumor;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We report a young girl who died in an Addisonian crisis due to previously undiagnosed congenital adrenal hyperplasia (CAH), in whom ovarian adrenal rest tissue was detected at postmortem histopathological examination. This is a very rare complication in female patients with CAH with only two previously reported cases.
引用
收藏
页码:177 / 182
页数:6
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