Oculopharyngeal muscular dystrophy: clinical and CT findings

被引：6

作者：

Bilgen, C ^{[1
]}

Bilgen, IG ^{[1
]}

Sener, RN ^{[1
]}

机构：

[1] Ege Univ, Sch Med, Dept Otorhinolaryngol, TR-35100 Izmir, Turkey

来源：

COMPUTERIZED MEDICAL IMAGING AND GRAPHICS | 2001年 / 25卷 / 06期

关键词：

oculopharyngeal muscular dystrophia; secretory otitis media; CT studies;

D O I：

10.1016/S0895-6111(01)00021-0

中图分类号：

R318 [生物医学工程];

学科分类号：

0831 ;

摘要：

A family affected with oculopharygeal muscular dystrophy (OPMD) is reported. This is an uncommon progressive myopathy. The proband presented for evaluation of secretory otitis media with effusion, as a result of tubal dysfunction. CT examination of the father revealed prominent muscular atrophy, and widespread fatty degeneration of the psoas, paraspinal, gluteal and femoral muscles. (C) 2001 Published by Elsevier Science Ltd.

引用

页码：527 / 529

页数：3

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