Cutaneous angiosarcoma in a patient with xeroderma pigmentosum

被引:5
作者
Arora, Raman [1 ]
Sharma, Alok [1 ]
Gupta, Ruchika [1 ]
Vijayaraghavan, M. [1 ]
机构
[1] All India Inst Med Sci, Dept Pathol, New Delhi 110029, India
关键词
Angiosarcoma; cutaneous; ultraviolet radiation; xeroderma pigmentosum;
D O I
暂无
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Xeroderma pigmentosum (XP) is a rare, autosomal recessive disorder characterized by photosensitivity, cutaneous pigmentary changes, premature skin ageing and development of various cutaneous and internal malignancies at an early age as a result of a defect in nucleotide excision repair following ultraviolet light exposure. Cutaneous angiosarcomas are aggressive neoplasms that are rarely associated with XP. In this communication, we report the case of a 40-year-old male patient with XP who developed an angiosarcoma of the face and discuss the implications of this association in view of recent developments in this field.
引用
收藏
页码:504 / 506
页数:3
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