Rupture of an Abdominal Aortic Aneurysm in a Young Man with Marfan Syndrome

被引：2

作者：

Pedersen, Maria Weinkouff ^{[1
]}

Khiem Dinh Huynh ^{[2
]}

Baandrup, Ulrik Thorngren ^{[3
]}

Nielsen, Dorte Guldbrand ^{[4
]}

Andersen, Niels Holmark ^{[1
]}

机构：

[1] Aalborg Univ Hosp, Dept Cardiol, Aalborg, Denmark

[2] Aalborg Univ Hosp, Dept Vasc Surg, Aalborg, Denmark

[3] North Denmark Reg Hosp, Dept Pathol, Hjorring, Denmark

[4] Aarhus Univ Hosp, Dept Cardiol, Aarhus, Denmark

来源：

ANNALS OF VASCULAR SURGERY | 2018年 / 48卷

关键词：

D O I：

10.1016/j.avsg.2017.10.024

中图分类号：

R61 [外科手术学];

学科分类号：

摘要：

Abdominal aortic aneurysms (AAAs) are very rare in Marfan syndrome. We present a case with a young nonsmoking and normotensive male with Marfan syndrome, who developed an infrarenal AAA that presented with rupture to the retroperitoneal cavity causing life-threatening bleeding shock. The patient had acute aortic surgery and survived. Five months before this incident, the patient had uneventful elective aortic root replacement (ad modum David) due to an enlarged aortic root. At that time, his abdominal aorta was assessed with a routine ultrasound scan that showed a normal-sized abdominal aorta. This documents that the aneurysm had evolved very rapidly despite young age and absence of risk factors.

引用

页码：252.e5 / 252.e8

页数：4

共 12 条

[1] Low wall shear stress predominates at sites of abdominal aortic aneurysm rupture [J].

Boyd, April J. ;

Kuhn, David C. S. ;

Lozowy, Richard J. ;

Kulbisky, Gordon P. .

JOURNAL OF VASCULAR SURGERY, 2016, 63 (06) :1613-1619

[2] Comparison of Hemodynamics After Aortic Root Replacement Using Valve-Sparing or Bioprosthetic Valved Conduit [J].

Collins, Jeremy D. ;

Semaan, Edouard ;

Barker, Alex ;

McCarthy, Patrick M. ;

Carr, James C. ;

Markl, Michael ;

Malaisrie, S. Chris .

ANNALS OF THORACIC SURGERY, 2015, 100 (05) :1556-1562

[3] Background differences in baseline and stimulated MMP levels influence abdominal aortic aneurysm susceptibility [J].

Dale, Matthew A. ;

Suh, Melissa K. ;

Zhao, Shijia ;

Meisinger, Trevor ;

Gu, Linxia ;

Swier, Vicki J. ;

Agrawal, Devendra K. ;

Greiner, Timothy C. ;

Carson, Jeffrey S. ;

Baxter, B. Timothy ;

Xiong, Wanfen .

ATHEROSCLEROSIS, 2015, 243 (02) :621-629

[4] The Risk for Type B Aortic Dissection in Marfan Syndrome [J].

den Hartog, Alexander W. ;

Franken, Romy ;

Zwinderman, Aeilko H. ;

Timmermans, Janneke ;

Scholte, Arthur J. ;

van den Berg, Maarten P. ;

de Waard, Vivian ;

Pals, Gerard ;

Mulder, Barbara J. M. ;

Groenink, Maarten .

JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 2015, 65 (03) :246-254

[5] 2014 ESC Guidelines on the diagnosis and treatment of aortic diseases [J].

Erbel, Raimund ;

Aboyans, Victor ;

Boileau, Catherine ;

Bossone, Eduardo ;

Di Bartolomeo, Roberto ;

Eggebrecht, Holger ;

Evangelista, Arturo ;

Falk, Volkmar ;

Frank, Herbert ;

Gaemperli, Oliver ;

Grabenwoeger, Martin ;

Haverich, Axel ;

Iung, Bernard ;

Manolis, Athanasios John ;

Meijboom, Folkert ;

Nienaber, Christoph A. ;

Roffi, Marco ;

Rousseau, Herve ;

Sechtem, Udo ;

Sirnes, Per Anton ;

von Allmen, Regula S. ;

Vrints, Christiaan J. M. .

EUROPEAN HEART JOURNAL, 2014, 35 (41) :2873-U93

[6] Aortic events in a nationwide Marfan syndrome cohort [J].

Groth, Kristian A. ;

Stochholm, Kirstine ;

Hove, Hanne ;

Kyhl, Kasper ;

Gregersen, Pernille A. ;

Vejlstrup, Niels ;

Ostergaard, John R. ;

Gravholt, Claus H. ;

Andersen, Niels H. .

CLINICAL RESEARCH IN CARDIOLOGY, 2017, 106 (02) :105-112

[7] Abdominal Aortic Aneurysm in Marfan Syndrome [J].

Hagerty, Tracy ;

Geraghty, Patrick ;

Braverman, Alan C. .

ANNALS OF VASCULAR SURGERY, 2017, 40 :294.e1-294.e6

[8] Consensus statement on surgical pathology of the aorta from the Society for Cardiovascular Pathology and the Association For European Cardiovascular Pathology: II. Noninflammatory degenerative diseases - nomenclature and diagnostic criteria [J].

Halushka, Marc K. ;

Angelini, Annalisa ;

Bartoloni, Giovanni ;

Basso, Cristina ;

Batoroeva, Lubov ;

Bruneval, Patrick ;

Buja, L. Maximilian ;

Butany, Jagdish ;

d'Amati, Giulia ;

Fallon, John T. ;

Gallagher, Patrick J. ;

Gittenberger-de Groot, Adriana C. ;

Gouveia, Rosa H. ;

Kholova, Ivana ;

Kelly, Karen L. ;

Leone, Ornella ;

Litovsky, Silvio H. ;

Maleszewski, Joseph J. ;

Miller, Dylan V. ;

Mitchell, Richard N. ;

Preston, Stephen D. ;

Pucci, Angela ;

Radio, Stanley J. ;

Rodriguez, E. Rene ;

Sheppard, Mary N. ;

Stone, James R. ;

Suvarna, S. Kim ;

Tan, Carmela D. ;

Thiene, Gaetano ;

Veinot, John P. ;

van der Wal, Allard C. .

CARDIOVASCULAR PATHOLOGY, 2016, 25 (03) :247-257

[9] The revised Ghent nosology for the Marfan syndrome [J].

Loeys, Bart L. ;

Dietz, Harry C. ;

Braverman, Alan C. ;

Callewaert, Bert L. ;

De Backer, Julie ;

Devereux, Richard B. ;

Hilhorst-Hofstee, Yvonne ;

Jondeau, Guillaume ;

Faivre, Laurence ;

Milewicz, Dianna M. ;

Pyeritz, Reed E. ;

Sponseller, Paul D. ;

Wordsworth, Paul ;

De Paepe, Anne M. .

JOURNAL OF MEDICAL GENETICS, 2010, 47 (07) :476-485

[10] Missed opportunities for the detection of abdominal aortic aneurysms [J].

MacDonald, A. J. ;

Faleh, O. ;

Welch, G. ;

Kettlewell, S. .

EUROPEAN JOURNAL OF VASCULAR AND ENDOVASCULAR SURGERY, 2008, 35 (06) :698-700

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