ROLE OF THE CFTR-ASSOCIATED LIGAND (CAL) IN ΔF508-CFTR TRAFFICKING AND CELL SURFACE EXPRESSION

被引:0
|
作者
Bergbower, E. A. [1 ,2 ]
Boinot, C. [1 ,3 ]
Guggino, W. B. [1 ]
Cebotaru, L. [1 ,3 ]
机构
[1] Johns Hopkins Univ, Sch Med, Dept Physiol, Baltimore, MD 21205 USA
[2] Johns Hopkins Univ, Sch Med, Cellular & Mol Med Grad Program, Baltimore, MD USA
[3] Johns Hopkins Univ, Sch Med, Dept Med, Div Gastroenterol, Baltimore, MD 21205 USA
关键词
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
38
引用
收藏
页码:205 / 206
页数:2
相关论文
共 50 条
  • [1] CFTR-ASSOCIATED LIGAND (CAL) BINDS CFTR AT THE GOLGI TO REDUCE CFTR EXPRESSION AT THE CELL SURFACE
    Lee, H.
    Cheng, J.
    Guggino, W. B.
    PEDIATRIC PULMONOLOGY, 2011, : 223 - 223
  • [2] Increased functional cell surface expression of CFTR and ΔF508-CFTR by the anthracycline doxorubicin
    Maitra, R
    Shaw, CM
    Stanton, BA
    Hamilton, JW
    AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY, 2001, 280 (05): : C1031 - C1037
  • [3] Role for phospholipid interactions in the trafficking defect of ΔF508-CFTR
    Eidelman, O
    BarNoy, S
    Razin, M
    Zhang, J
    McPhie, P
    Lee, G
    Huang, Z
    Sorscher, EJ
    Pollard, HB
    BIOCHEMISTRY, 2002, 41 (37) : 11161 - 11170
  • [4] The CFTR-Associated Ligand Arrests the Trafficking of the Mutant ΔF508 CFTR Channel in the ER Contributing to Cystic Fibrosis
    Bergbower, Emily
    Boinot, Clement
    Sabirzhanova, Inna
    Guggino, William
    Cebotaru, Liudmila
    CELLULAR PHYSIOLOGY AND BIOCHEMISTRY, 2018, 45 (02) : 639 - 655
  • [5] The effects of curcumin on the expression of ΔF508-CFTR
    Weiner, SA
    Pearson, MA
    Geibel, JP
    Caplan, MJ
    Egan, ME
    PEDIATRIC RESEARCH, 2003, 53 (04) : 568A - 569A
  • [6] Correction of ΔF508-CFTR trafficking defect by deoxyspergualin.
    Jiang, C
    Xiao, Y
    Fang, S
    Nadler, SG
    Lee, D
    Jefferson, D
    Kaplan, J
    Smith, AE
    Cheng, SH
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 1999, 159 (03) : A679 - A679
  • [7] COMPETITIVE INHIBITORS OF CAL STABILIZE ΔF508-CFTR AT THE APICAL MEMBRANE
    Cushing, P.
    Boisguerin, P.
    Vouilleme, L.
    Pellegrini, M.
    Mierke, D.
    Smithson, D.
    Guy, R.
    Madden, D. R.
    PEDIATRIC PULMONOLOGY, 2009, : 224 - 224
  • [8] RESTORING ΔF508-CFTR TRAFFICKING AND ACTIVITY WITH EPIGENETIC MODIFIERS
    Hutt, D. M.
    Herman, D. M.
    Rodrigues, A. P.
    Noel, S.
    Gentzsch, M.
    Pilewski, J. M.
    Riordan, J. R.
    Sorscher, E. J.
    Kelly, J. W.
    Frizzell, R. A.
    Manning, G.
    Gottesfeld, J. M.
    Balch, W. E.
    PEDIATRIC PULMONOLOGY, 2009, : 215 - 215
  • [9] Designing CAL-selective PDZ inhibitors:: A pharmacological approach to stabilizing ΔF508-CFTR at the cell surface
    Cushing P. R.
    Fellows A.
    Coutermarsh B.
    Talebian L.
    Stanton B. A.
    Wolde M.
    Cheng J.
    Guggino W. B.
    Boisguerin P.
    Mierke D. F.
    Madden D. R.
    PEDIATRIC PULMONOLOGY, 2007, : 215 - 216
  • [10] Trafficking of ΔF508-CFTR to the plasma membrane in polarized epithelial cells
    Stanton, BA
    Loffing-Cueni, D
    Loffing, J
    FASEB JOURNAL, 2000, 14 (04): : A101 - A101