Association of atrial septal defect with poland-moebius syndrome: Vascular disruption cad be a common etiologic factor - A case report

被引:15
作者
Matsui, A [1 ]
Nakagawa, M [1 ]
Okuno, M [1 ]
机构
[1] SHIGA UNIV MED SCI,DEPT PEDIAT,OTSU,SHIGA 52021,JAPAN
关键词
D O I
10.1177/000331979704800311
中图分类号
R6 [外科学];
学科分类号
1002 ; 100210 ;
摘要
The authors describe an association of atrial septal defect with partial symptoms of the Poland-Moebius syndrome. Both are thought to be caused by developmental disorders of the mesenchyme and ectodermal derivatives. This anomalous association can be accepted as one concept of the subclavian artery blood supply disruption sequence during embryogenesis.
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页码:269 / 271
页数:3
相关论文
共 6 条
  • [1] ASAMI I, 1995, DEVELOPMENTAL MECHANISMS OF HEART DISEASE, P255
  • [2] SUBCLAVIAN ARTERY SUPPLY DISRUPTION SEQUENCE - HYPOTHESIS OF A VASCULAR ETIOLOGY FOR POLAND, KLIPPEL-FEIL, AND MOBIUS ANOMALIES
    BAVINCK, JNB
    WEAVER, DD
    [J]. AMERICAN JOURNAL OF MEDICAL GENETICS, 1986, 23 (04): : 903 - 918
  • [3] STUDIES OF MALFORMATION SYNDROMES OF MAN XXXXI B - NOSOLOGIC STUDIES IN HANHART-SYNDROME AND MOBIUS SYNDROME
    HERRMANN, J
    PALLISTER, PD
    GILBERT, EF
    VISESKUL, C
    BERSU, E
    PETTERSEN, JC
    OPITZ, JM
    [J]. EUROPEAN JOURNAL OF PEDIATRICS, 1976, 122 (01) : 19 - 55
  • [4] NAKAGAWA M, 1993, ANAT EMBRYOL, V187, P445
  • [5] ASYMMETRIC CRYING FACIES - INDEX OF OTHER CONGENITAL ANOMALIES
    PAPE, KE
    PICKERING, D
    [J]. JOURNAL OF PEDIATRICS, 1972, 81 (01) : 21 - +
  • [6] ASSOCIATION OF ATRIAL SEPTAL-DEFECT WITH POLANDS SYNDROME
    SAMANT, AR
    DESSER, KB
    BENCHIMOL, A
    [J]. AMERICAN HEART JOURNAL, 1983, 106 (01) : 159 - 161