Valvular Heart Disease in Patients with Osteogenesis Imperfecta

被引:13
作者
Najib, Mohammad Q. [1 ]
Schaff, Hartzell V. [2 ]
Ganji, Jhansi [1 ]
Lee, Howard R. [1 ]
Click, Roger L. [3 ]
Miller, D. Craig [4 ]
Chaliki, Hari P. [1 ]
机构
[1] Mayo Clin, Div Cardiovasc Dis, Scottsdale, AZ 85259 USA
[2] Mayo Clin, Div Cardiovasc Surg, Rochester, MN USA
[3] Mayo Clin, Div Cardiovasc Dis, Rochester, MN USA
[4] Stanford Univ, Div Cardiovasc Surg, Stanford, CA 94305 USA
关键词
AORTIC DISSECTION; REGURGITATION; REPLACEMENT; INVOLVEMENT;
D O I
10.1111/jocs.12064
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Osteogenesis imperfecta (OI) or brittle bone disease is a rare connective tissue hereditary disorder. The most common clinical presentation of OI is bone fractures. OI also involves extraskeletal structures; however, cardiovascular manifestations are rare. In this report, we describe the cardiovascular anomalies of patients with OI who underwent valve surgery and review the literature on this subject. doi: 10.1111/jocs.12064 (J Card Surg 2013;28:139143)
引用
收藏
页码:139 / 143
页数:5
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