Congenital Heart Disease and Pulmonary Hypertension

被引:13
作者
Constantine, Andrew [1 ,2 ,3 ]
Dimopoulos, Konstantinos [1 ,2 ,3 ]
Opotowsky, Alexander R. [4 ]
机构
[1] Royal Brompton & Harefield NHS Fdn Trust, Royal Brompton Hosp, Adult Congenital Heart Ctr, Sydney St, London SW3 6NP, England
[2] Royal Brompton & Harefield NHS Fdn Trust, Royal Brompton Hosp, Natl Ctr Pulm Hypertens, Sydney St, London SW3 6NP, England
[3] Imperial Coll London, Natl Heart & Lung Inst, Guy Scadding Bldg,Cale St, London SW3 6LY, England
[4] Univ Cincinnati, Cincinnati Childrens Hosp, Dept Pediat, Heart Inst,Coll Med, Cincinnati, OH 45229 USA
关键词
Pulmonary hypertension; Adult congenital heart disease; Precapillary; Postcapillary; Echocardiography; Cardiac catheterization; Eisenmenger syndrome; VENTRICULAR SEPTAL-DEFECTS; ARTERIAL-HYPERTENSION; EISENMENGER-SYNDROME; EXERCISE CAPACITY; DOUBLE-BLIND; FONTAN PATIENTS; ADULTS; BOSENTAN; THERAPY; IMPACT;
D O I
10.1016/j.ccl.2020.04.008
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Pulmonary hypertension (PH) is common in adults with congenital heart disease and carries fundamental implications for management and prognosis. A high index of suspicion, combined with knowledge of the pathogenesis and pathophysiology of PH, is required to achieve a timely, accurate diagnosis, and appropriate classification and treatment. This article provides a guide on how to approach the adult with congenital heart disease and suspected PH of different types, including current management.
引用
收藏
页码:445 / +
页数:13
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