Electrocardiographic Predictors of Electroanatomic Scar Size in Arrhythmogenic Right Ventricular Cardiomyopathy: Implications for Arrhythmic Risk Stratification
ECG Predictors of Electroanatomic Scar in ARVC IntroductionThe extent of right ventricular (RV) electroanatomic scar (EAS) detected by endocardial voltage mapping (EVM) is a powerful invasive predictor of arrhythmic outcome in patients with arrhythmogenic right ventricular cardiomyopathy (ARVC). Electrocardiogram (ECG) and signal-averaged ECG are noninvasive tools of established clinical value for the diagnosis of electrical abnormalities in ARVC. This study was designed to assess the role of ECG and SAECG abnormalities for noninvasive estimation of the extent and regional distribution of RV-EAS and prediction of scar-related arrhythmic risk. Methods and ResultsThe study population included 49 consecutive patients (38 males, median age 35 years) with a definite diagnosis of ARVC and an abnormal EVM by CARTO system. At univariate analysis, the presence of epsilon waves, the degree of RV dilation, the severity of RV dysfunction, and the extent of negative T waves correlated with RV-EAS% area. Normal T-waves were associated with a median RV-EAS% area of 4.9% (4.5-6.4), negative T waves in V1-V3 of 22.0% (8.5-30.6), negative T waves in V1-V3 extending to lateral precordial leads (V4-V6) of 26.8% (11.5-35.2), and negative T waves in both precordial (V2-V6) and inferior leads of 30.2% (24.8-33.0) (P < 0.001). At multivariate analysis, the extent of negative T waves remained the only independent predictor of RV-EAS% area (B = 4.4, 95%CI 1.3-7.4, P = 0.006) and correlated with the arrhythmic event-rate during follow-up (P = 0.03). ConclusionsIn patients with ARVC, the extent of negative T-waves across 12-lead ECG allows noninvasive estimation of the amount of RV-EAS and prediction of EAS-related arrhythmic risk.
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Taipei Vet Gen Hosp, Yuanshan Branch, Div Cardiol, Yi Lan, Taiwan
Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
Natl Yang Ming Univ, Cardiovasc Res Inst, Taipei 112, TaiwanTaipei Vet Gen Hosp, Div Cardiol, Taipei, Taiwan
Li, Cheng-Hung
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Lin, Yenn-Jiang
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Taichung Vet Gen Hosp, Div Cardiol, Taichung, TaiwanTaipei Vet Gen Hosp, Div Cardiol, Taipei, Taiwan
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Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Taichung Vet Gen Hosp, Div Cardiol, Taichung, TaiwanTaipei Vet Gen Hosp, Div Cardiol, Taipei, Taiwan
Wu, Tsu-Juey
Cheng, Chen-Chuan
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Taipei Vet Gen Hosp, Div Cardiol, Taipei, Taiwan
Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Tuan, Ta-Chuan
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Chang, Shih-Lin
Lo, Li-Wei
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Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Lo, Li-Wei
Hu, Yu-Feng
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Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Hu, Yu-Feng
Chao, Tze-Fan
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Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Chao, Tze-Fan
Chung, Fa-Po
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Tsao, Hsuan-Ming
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Natl Yang Ming Univ Hosp, Div Cardiol, Yi Lan, Taiwan
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Tsao, Hsuan-Ming
Chen, Shih-Ann
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Taipei Vet Gen Hosp, Div Cardiol, Taipei, Taiwan
Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Univ Penn Hlth Syst, Div Cardiol, Electrophysiol Sect, Philadelphia, PA USAUniv Penn Hlth Syst, Div Cardiol, Electrophysiol Sect, Philadelphia, PA USA
Marchlinski, FE
Zado, E
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Dixit, S
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Gerstenfeld, E
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Callans, DJ
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Hsia, H
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Pulliam, W
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Taipei Vet Gen Hosp, Yuanshan Branch, Div Cardiol, Yi Lan, Taiwan
Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Li, Cheng-Hung
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Wu, Tsu-Juey
Cheng, Chen-Chuan
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Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Tuan, Ta-Chuan
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Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Lo, Li-Wei
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Hu, Yu-Feng
Chao, Tze-Fan
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Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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Chao, Tze-Fan
Chung, Fa-Po
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Tsai, Chin-Feng
Tsao, Hsuan-Ming
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Tsao, Hsuan-Ming
Chen, Shih-Ann
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Natl Yang Ming Univ, Inst Clin Med, Taipei 112, Taiwan
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机构:
Univ Penn Hlth Syst, Div Cardiol, Electrophysiol Sect, Philadelphia, PA USAUniv Penn Hlth Syst, Div Cardiol, Electrophysiol Sect, Philadelphia, PA USA
Marchlinski, FE
Zado, E
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Dixit, S
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Gerstenfeld, E
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Callans, DJ
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Hsia, H
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Hsia, H
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Lin, D
Nayak, H
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Pulliam, W
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