Small-cell carcinoma of the ovary of the hypercalcemic type in an 8-year-old girl

被引:9
作者
Schleef, J [1 ]
Wagner, A [1 ]
Kleta, R [1 ]
Schaarschmidt, K [1 ]
Dockhorn-Dworniczak, B [1 ]
Willital, GH [1 ]
Jürgens, H [1 ]
机构
[1] WW Univ Munster, Dept Pediat Hematol & Oncol, Munster, Germany
关键词
ovarian tumor; children; hypercalcemia; small-cell carcinoma;
D O I
10.1007/s003830050625
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Tumors of the ovary in girls represent about 80% of pediatric genital tumors; approximately 30% of these tumors are malignant. The risk of malignancy increases with decreasing age. The most frequent finding is a teratoma; other tumors are rare. Small-cell carcinoma (SCCO) of the ovary is extremely rare, occurring mostly in young women. We present an 8-year-old girl with a SCCO of the hypercalcemic type. The findings and treatment are discussed with emphasis on the poor prognosis in these patients, even in stage 1 disease. The current literature is reviewed.
引用
收藏
页码:431 / 434
页数:4
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