Pectus excavatum: Pathophysiology and clinical characteristics

被引:48
作者
Koumbourlis, Anastassios C. [1 ]
机构
[1] Schneider Childrens Hosp, N Shore Long Isl Jewish Hlth Syst, Albert Einstein Coll Med, Div Pediat Pulm Med, Great Neck, NY 11021 USA
关键词
Pectus excavatum; Chest wall deformity; Exercise intolerance; Lung function; PULMONARY-FUNCTION; CARDIORESPIRATORY FUNCTION; CORRECTIVE SURGERY; NUSS PROCEDURE; REPAIR; LUNG; EXERCISE; CHILDREN;
D O I
10.1016/j.prrv.2008.12.002
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Pectus Excavatum is the most common congenital abnormality of the chest wall. In the majority of the cases the condition is idiopathic. Affected patients tend to have lung volumes that are mildly decreased but within the normal range and they are often associated with mild air-trapping. Many patients show evidence of lower airway obstruction. Exercise intolerance is the most common symptom associated with pectus excavatum, and it is now believed to be due to cardiovascular rather than pulmonary causes. The psychological effect of the deformity often exceeds its actual physical effect. Several surgical techniques are available for the repair of the deformity, although the need for it is still considered controversial by many. The current article provides an in depth review of the pathophysiology and clinical characteristics of pectus excavatum, as well as an overview of the treatment options in order to help the practitioners caring of affected patients in their evaluation. (C) 2009 Elsevier Ltd All rights reserved.
引用
收藏
页码:3 / 6
页数:4
相关论文
共 23 条
[1]   Lung function after the minimal invasive pectus excavatum repair (Nuss procedure) [J].
Aronson, Daniel C. ;
Bosgraaf, Remko P. ;
Merz, Eva-Maria ;
van Steenwijk, Reindert P. ;
van Aalderen, Wim M. C. ;
van Baren, Robertine .
WORLD JOURNAL OF SURGERY, 2007, 31 (07) :1518-1522
[2]   Pulmonary function and exercise response in patients with pectus excavatum after nuss repair [J].
Borowitz, D ;
Cerny, F ;
Zallen, G ;
Sharp, J ;
Burke, M ;
Gross, K ;
Glick, PL .
JOURNAL OF PEDIATRIC SURGERY, 2003, 38 (04) :544-547
[3]  
Chung C S, 1975, Birth Defects Orig Artic Ser, V11, P1
[4]  
FOLKALSRUD EW, 2004, AM J SURG, V187, P192
[5]   Current management of pectus excavatum [J].
Fonkalsrud, EW .
WORLD JOURNAL OF SURGERY, 2003, 27 (05) :502-508
[6]   Thoracic deformities and the growing lung [J].
Grissom, LE ;
Harcke, HT .
SEMINARS IN ROENTGENOLOGY, 1998, 33 (02) :199-208
[7]   Chest wall constriction after too extensive and too early operations for pectus excavatum [J].
Haller, JA ;
Colombani, PM ;
Humphries, CT ;
Azizkhan, RG ;
Loughlin, GM .
ANNALS OF THORACIC SURGERY, 1996, 61 (06) :1618-1624
[8]   USE OF CT SCANS IN SELECTION OF PATIENTS FOR PECTUS EXCAVATUM SURGERY - A PRELIMINARY-REPORT [J].
HALLER, JA ;
KRAMER, SS ;
LIETMAN, SA .
JOURNAL OF PEDIATRIC SURGERY, 1987, 22 (10) :904-906
[9]  
Haller JA, 2000, J CARDIOVASC SURG, V41, P125
[10]  
KAGURAOKA H, 1992, J THORAC CARDIOV SUR, V104, P1483