Bernard-Soulier syndrome in pregnancy

被引：18

作者：

Prabu, P. ^{[1
]}

Parapia, L. A. ^{[1
]}

机构：

[1] Bradford Teaching Hosp NHS Trust, Haemophilia Ctr, Bradford BD9 6RJ, W Yorkshire, England

来源：

CLINICAL AND LABORATORY HAEMATOLOGY | 2006年 / 28卷 / 03期

关键词：

Bernard-Soulier syndrome; platelet disorder; pregnancy;

D O I：

10.1111/j.1365-2257.2006.00780.x

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Bernard-Soulier syndrome (BSS) is a rare autosomal recessively inherited bleeding disorder. Pregnancy in patients with BSS is characterized by ante-, intra-, or postpartum haemorrhage, which may be delayed and severe. There is no consensus in the management of BSS in pregnancy and so far only 16 pregnancies in nine patients have been described. We report a further three pregnancies in two women with the syndrome. We also outline our management of pregnant patients with BSS.

引用

页码：198 / 201

页数：4

共 27 条

[1] The use of recombinant factor VIIa in children with inherited platelet function disorders [J].

Almeida, AM ;

Khair, K ;

Hann, I ;

Liesner, R .

BRITISH JOURNAL OF HAEMATOLOGY, 2003, 121 (03) :477-481

[2]

AVILA M A, 1992, Journal de Gynecologie Obstetrique et biologie de la Reproduction, V21, P73

[3]

Bernard J, 1996, CR ACAD SCI III-VIE, V319, P727

[4]

BERNARD J, 1948, SEMINALE HOPITAUX PA, V244, P159

[5] The molecular mechanism of platelet adhesion [J].

Berndt, MC ;

Ward, CM ;

DeLuca, M ;

Facey, DA ;

Castaldi, PA ;

Harris, SJ ;

Andrews, RK .

AUSTRALIAN AND NEW ZEALAND JOURNAL OF MEDICINE, 1995, 25 (06) :822-830

[6]

BERNDT MC, 1983, BLOOD, V62, P800

[7] PARTIAL EXPRESSION OF GP-IB MEASURED BY FLOW-CYTOMETRY IN 2 PATIENTS WITH BERNARD-SOULIER-SYNDROME [J].

BUNESCU, A ;

LINDAHL, T ;

SOLUM, NO ;

SCHULMAN, S ;

LARSSON, A ;

LUNDAHL, J ;

EGBERG, N .

THROMBOSIS RESEARCH, 1994, 76 (05) :441-450

[8] CHARACTERIZATION OF THE PLATELET MEMBRANE GLYCOPROTEIN ABNORMALITIES IN BERNARD-SOULIER SYNDROME AND COMPARISON WITH NORMAL BY SURFACE-LABELING TECHNIQUES AND HIGH-RESOLUTION TWO-DIMENSIONAL GEL-ELECTROPHORESIS [J].

CLEMETSON, KJ ;

MCGREGOR, JL ;

JAMES, E ;

DECHAVANNE, M ;

LUSCHER, EF .

JOURNAL OF CLINICAL INVESTIGATION, 1982, 70 (02) :304-311

[9] DDAVP SHORTENS THE BLEEDING-TIME IN BERNARD-SOULIER SYNDROME [J].

CUTHBERT, RJG ;

WATSON, HHK ;

HANDA, SI ;

ABBOTT, I ;

LUDLAM, CA .

THROMBOSIS RESEARCH, 1988, 49 (06) :649-650

[10] Antepartum diagnosis of fetal intracranial hemorrhage due to maternal Bernard-Soulier syndrome [J].

Fujimori, K ;

Ohto, H ;

Honda, S ;

Sato, A .

OBSTETRICS AND GYNECOLOGY, 1999, 94 (05) :817-819

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