Cardiac sarcoidosis presenting as arrhythmogenic right ventricular cardiomyopathy/dysplasia with ventricular aneurysms: a case report

被引：6

作者：

Petrovic, Marija ^{[1
]}

Buja, L. Maximilian ^{[2
]}

Kar, Biswajit ^{[1
]}

Colnaric, Jure ^{[1
]}

Damaraju, Sarita ^{[1
]}

Zhao, Bihong ^{[2
]}

Akkanti, Bindu ^{[1
]}

Radovanovic, Milan ^{[1
]}

Radovancevic, Rajko ^{[1
]}

Loyalka, Pranav ^{[1
]}

Gregoric, Igor D. ^{[1
]}

机构：

[1] Univ Texas Hlth Sci Ctr Houston, Mem Hermann Hosp, Texas Med Ctr, Ctr Adv Heart Failure, 6400 Fannin St,Suite 2350, Houston, TX 77030 USA

[2] Univ Texas Hlth Sci Ctr Houston, Mem Hermann Hosp, Texas Med Ctr, Dept Pathol & Lab Med, 6431 Fannin St, Houston, TX 77030 USA

来源：

CARDIOVASCULAR PATHOLOGY | 2018年 / 33卷

关键词：

Cardiac sarcoidosis; ARVD; Ventricular aneurysms; Heart transplantation; HEART-TRANSPLANTATION; END-STAGE; MYOCARDITIS; DIAGNOSIS; CRITERIA; CURE;

D O I：

10.1016/j.carpath.2017.11.001

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A 70-year old Caucasian man with recurrent ventricular tachycardia and progressive biventricular failure attributed to arrhythmogenic right ventricular cardiomyopathy/dysplasiawas evaluated for heart transplantation. Cardiac ventriculography revealed an abnormal left ventricle with five saccular aneurysms. Heart transplantation was performed. Pathology of the explanted heart showed multifocal sarcoid granulomas. Replacement fibrosis was widespread in both ventricles and associated with saccular aneurysms. No genetic basis was identified. Thus, the evidence suggested progressive cardiac sarcoidosis caused this patient's unusual condition. (c) 2017 Published by Elsevier Inc.

引用

页码：1 / 5

页数：5

共 23 条

[1] Altered Desmosomal Proteins in Granulomatous Myocarditis and Potential Pathogenic Links to Arrhythmogenic Right Ventricular Cardiomyopathy [J].