Pulmonary arterial hypertension masquerading as severe refractory asthma

被引：24

作者：

Achouh, L. ^{[1
]}

Montani, D. ^{[1
]}

Garcia, G. ^{[1
]}

Jais, X. ^{[1
]}

Hamid, A. M. ^{[1
]}

Mercler, O. ^{[2
]}

Simonneau, G. ^{[1
]}

Humbert, M. ^{[1
]}

机构：

[1] Univ Paris 11, Hop Antoine Beclere, Ctr Natl Reference Hypertens Arterielle Pulmonair, Serv Pneumol & Reanimat Resp, F-92140 Clamart, France

[2] Univ Paris 11, Ctr Chirurg Marie Lannelongue, Serv Chirurg Thorac, Le Plessis Robinson, France

来源：

EUROPEAN RESPIRATORY JOURNAL | 2008年 / 32卷 / 02期

关键词：

asthma; compression of the mainstem bronchi; congenital heart diseases; obstructive airway disease; Ortner's syndrome; pulmonary arterial hypertension;

D O I：

10.1183/09031936.00005408

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

Once the diagnosis of pulmonary arterial hypertension is established, wheezing and chronic cough are rarely described during the course of the disease. The present study reports on two nonsmoking patients with severe pulmonary arterial hypertension, confirmed by right-heart catheterisation, who developed chronic cough, wheezing and irreversible obstructive lung disease masquerading as adult-onset severe refractory asthma. In both cases, extrinsic proximal airway obstruction by dilated pulmonary arteries was demonstrated by fibreoptic bronchoscopy and computed tomography of the chest. The present observations add dilatation of the central pulmonary arteries with compression of the mainstem bronchi to the list of masqueraders of asthma in patients with pulmonary arterial hypertension.

引用

页码：513 / 516

页数：4

共 17 条

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