Coexistence of left ventricular noncompaction and double-orifice mitral valve in a patient with congestive heart failure
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Demir, Fikri
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Ankara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, TurkeyAnkara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, Turkey
Demir, Fikri
[1
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Atalay, Semra
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Ankara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, TurkeyAnkara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, Turkey
Atalay, Semra
[1
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Karadeniz, Cem
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Ankara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, TurkeyAnkara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, Turkey
Karadeniz, Cem
[1
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Tutar, Ercan
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Ankara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, TurkeyAnkara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, Turkey
Tutar, Ercan
[1
]
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[1] Ankara Univ, Fac Med, Dept Pediat, Div Pediat Cardiol, TR-06100 Ankara, Turkey
Left ventricular noncompaction (LVNC) is a rare cardiomyopathy. It usually presents with ventricular dysfunction, thromboembolic events and arrhythmias. An asymptomatic clinical course is also possible. LVNC is frequently associated with other congenital heart diseases including heart valve abnormalities. The coexistence of LVNC with double-orifice mitral valve was observed rarely. The presence of such coexistence in a patient presented with heart failure in the newborn period is reported herein because of its rarity.