Cognitive abilities in Williams syndrome

被引:18
作者
Miezah, Daniel [1 ]
Porter, Melanie [1 ]
Batchelor, Jennifer [1 ]
Boulton, Kelsie [1 ]
Veloso, Gabrielle Campos [1 ]
机构
[1] Macquarie Univ, Psychol Dept, Herring Rd, Sydney, NSW 2109, Australia
关键词
Williams syndrome; Cognitive abilities; Cognitive heterogeneity; Cognitive homogeneity; BEUREN-SYNDROME; DOWN-SYNDROME; PHENOTYPE; CHILDREN; HETEROGENEITY; INDIVIDUALS; STRENGTHS; ADULTS; SKILLS;
D O I
10.1016/j.ridd.2020.103701
中图分类号
G76 [特殊教育];
学科分类号
040109 ;
摘要
The current study utilized a comprehensive neuropsychological test battery to investigate cognitive abilities in a sample of 49 WS individuals (25 male) aged 6-39 years. Age effects were also investigated by splitting the sample into child and adult groups. Cognitive heterogeneity was found on the Woodcock Johnson III Tests of Cognitive Abilities, Australian Adaptation (WJ-III COG) (Woodcock, McGrew, & Mather, 2001), with cognitive abilities ranging from profoundly impaired to superior and individualized profiles of strength and weakness varying considerably. Overall, findings supported previous research showing strengths in auditory processing and phonemic awareness. The weakest performance, on average, was in processing speed, attention, delayed associative learning and executive functioning capabilities. Visual-spatial functioning was not a weakness overall, neither was nonverbal reasoning. Chronological age did not relate significantly to cognitive abilities. Findings highlight the need for individual assessment and management of WS individuals.
引用
收藏
页数:13
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共 69 条
  • [1] [Anonymous], THESIS
  • [2] [Anonymous], 1965, THESIS
  • [3] BELLUGI U, 1990, AM J MED GENET, P115
  • [4] The neurocognitive profile of Williams syndrome: A complex pattern of strengths and weaknesses
    Bellugi, U
    Lichtenberger, L
    Jones, W
    Lai, Z
    St George, M
    [J]. JOURNAL OF COGNITIVE NEUROSCIENCE, 2000, 12 : 7 - 29
  • [5] Parieto-occipital grey matter abnormalities in children with Williams syndrome
    Boddaert, N
    Mochel, F
    Meresse, I
    Seidenwurm, D
    Cachia, A
    Brunelle, F
    Lyonnet, S
    Zbovicius, M
    [J]. NEUROIMAGE, 2006, 30 (03) : 721 - 725
  • [6] Adaptive functioning in Williams syndrome and its relation to demographic variables and family environment
    Brawn, Gabrielle
    Porter, Melanie
    [J]. RESEARCH IN DEVELOPMENTAL DISABILITIES, 2014, 35 (12) : 3606 - 3623
  • [7] Language abilities in Williams syndrome: A critical review
    Brock, Jon
    [J]. DEVELOPMENT AND PSYCHOPATHOLOGY, 2007, 19 (01) : 97 - 127
  • [8] Williams syndrome: Pediatric, neurologic, and cognitive development
    Carrasco, X
    Castillo, S
    Aravena, T
    Rothhammer, P
    Aboitiz, F
    [J]. PEDIATRIC NEUROLOGY, 2005, 32 (03) : 166 - 172
  • [9] Carroll B J., 1993, Human cognitive abilities: A survey of factor-analytical studies
  • [10] Cattell R.B., 1941, PSYCHOL BULL, V38, P592