Diagnosis and classification of adult Still's disease

被引:57
作者
Mahroum, Naim [1 ]
Mahagna, Hussein [1 ]
Amital, Howard [1 ]
机构
[1] Tel Aviv Univ, Sackler Fac Med, Sheba Med Ctr, Dept Med B, IL-69978 Tel Aviv, Israel
关键词
Still's disease; Fever; Arthritis; Rash; fever of unknown origin; Cytokines; JUVENILE IDIOPATHIC ARTHRITIS; CRITERIA; INFECTION; ANAKINRA; FERRITIN; FRANCE;
D O I
10.1016/j.jaut.2014.01.011
中图分类号
R392 [医学免疫学]; Q939.91 [免疫学];
学科分类号
100102 ;
摘要
The cornerstone of adult onset Still's disease is the triad of daily fever, arthritis and rash. This syndrome remains enigmatic and most often a disease of exclusion. There are both musculoskeletal as well as systemic features. More importantly, reactive hemophagocytic syndrome may occur in patients. In this review we attempt to place this syndrome in perspective, including data on geoepidemiology, clinical and laboratory features. (C) 2014 Elsevier Ltd. All rights reserved.
引用
收藏
页码:34 / 37
页数:4
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