Ataxin-3, a nucleocytoplasmic shuttling protease: implications for Machado-Joseph disease

被引:0
|
作者
不详
机构
来源
BIOCHEMISTRY AND CELL BIOLOGY-BIOCHIMIE ET BIOLOGIE CELLULAIRE | 2005年 / 83卷 / 06期
关键词
D O I
暂无
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:777 / 777
页数:1
相关论文
共 50 条
  • [31] Motor uncoordination and neuropathology in a transgenic mouse model of Machado-Joseph disease lacking intranuclear inclusions and ataxin-3 cleavage products
    Silva-Fernandes, Anabela
    Costa, Maria do Carmo
    Duarte-Silva, Sara
    Oliveira, Pedro
    Botelho, Claudia M.
    Martins, Luis
    Mariz, Jose Antonio
    Ferreira, Tiago
    Ribeiro, Filipa
    Correia-Neves, Margarida
    Costa, Cristina
    Maciel, Patricia
    NEUROBIOLOGY OF DISEASE, 2010, 40 (01) : 163 - 176
  • [32] Towards a structural understanding of the fibrillization pathway in Machado-Joseph's disease: Trapping early oligomers of non-expanded ataxin-3
    Gales, L
    Cortes, L
    Almeida, C
    Melo, CV
    Costa, MD
    Maciel, P
    Clarke, DT
    Damas, AM
    Macedo-Ribeiro, S
    JOURNAL OF MOLECULAR BIOLOGY, 2005, 353 (03) : 642 - 654
  • [33] MACHADO-JOSEPH DISEASE
    SUDARSKY, L
    COUTINHO, P
    CLINICAL NEUROSCIENCE, 1995, 3 (01) : 17 - 22
  • [34] MACHADO-JOSEPH DISEASE OR NOT
    DAWSON, DM
    ARCHIVES OF NEUROLOGY, 1991, 48 (06) : 570 - 570
  • [35] Excitation-induced ataxin-3 aggregation in neurons from patients with Machado–Joseph disease
    Philipp Koch
    Peter Breuer
    Michael Peitz
    Johannes Jungverdorben
    Jaideep Kesavan
    Daniel Poppe
    Jonas Doerr
    Julia Ladewig
    Jerome Mertens
    Thomas Tüting
    Per Hoffmann
    Thomas Klockgether
    Bernd O. Evert
    Ullrich Wüllner
    Oliver Brüstle
    Nature, 2011, 480 : 543 - 546
  • [36] A mutant ataxin-3 putative-cleavage fragment in brains of Machado-Joseph disease patients and transgenic mice is cytotoxic above a critical concentration
    Goti, D
    Katzen, SM
    Mez, J
    Kurtis, N
    Kiluk, J
    Ben-Haïem, L
    Jenkins, NA
    Copeland, NG
    Kakizuka, A
    Sharp, AH
    Ross, CA
    Mouton, PR
    Colomer, V
    JOURNAL OF NEUROSCIENCE, 2004, 24 (45): : 10266 - 10279
  • [37] Serotonergic signalling suppresses ataxin 3 aggregation and neurotoxicity in animal models of Machado-Joseph disease
    Teixeira-Castro, Andreia
    Jalles, Ana
    Esteves, Sofia
    Kang, Soosung
    Santos, Liliana da Silva
    Silva-Fernandes, Anabela
    Neto, Mario F.
    Brielmann, Renee M.
    Bessa, Carlos
    Duarte-Silva, Sara
    Miranda, Adriana
    Oliveira, Stephanie
    Neves-Carvalho, Andreia
    Bessa, Joao
    Summavielle, Teresa
    Silverman, Richard B.
    Oliveira, Pedro
    Morimoto, Richard I.
    Maciel, Patricia
    BRAIN, 2015, 138 : 3221 - 3237
  • [38] Genetics of Machado-Joseph disease
    Sequeiros, J
    EUROPEAN JOURNAL OF HUMAN GENETICS, 1998, 6 : 23 - 23
  • [39] Identification of the calpain-generated toxic fragment of ataxin-3 protein provides new avenues for therapy of Machado-Joseph disease| Spinocerebellar ataxia type 3
    Simoes, Ana Teresa
    Carmona, Vitor
    Duarte-Neves, Joana
    Cunha-Santos, Janete
    de Almeida, Luis Pereira
    NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY, 2022, 48 (01)
  • [40] Tremulous Machado-Joseph Disease
    Procaci, V.
    de Farias, L.
    da Costa, S.
    Barsottini, O.
    Pedroso, J.
    MOVEMENT DISORDERS, 2024, 39 : S625 - S625