Pulmonary Arterial Hypertension

Pulmonary hypertension (PH) is a rare, complex, life-threatening disorder. Most patients present with vague symptoms, making early diagnosis very difficult. Pulmonary arterial hypertension, a category of PH, is characterized by vascular proliferation and remodeling. It causes progressive increase in pulmonary vascular resistance resulting in right ventricular. failure and death. Treatment options targeting specific pathways for patients with the disease have evolved in the last 20 years to help improve quality of life and prolong their survival. The purpose of this article is to provide an insightful and helpful review of the classification of pulmonary hypertension, assessment, and treatment options.