Pleuropulmonary blastoma: 4 cases

被引:0
作者
Benouachane, T [1 ]
El Khorassani, M [1 ]
Nachef, MN [1 ]
Khattab, M [1 ]
Alhamany, Z [1 ]
Barahioui, M [1 ]
Alaoui, FM [1 ]
机构
[1] Hop Enfants, Serv Pediat Hematooncol 2, Rabat, Morocco
关键词
pleuropulmonary blastoma; pulmonary tumor; child; pneumonectomy;
D O I
暂无
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Pleuropulmonary blastoma is an uncommon malignant lung tumor observed in children. Outcome is often unfavorable. Two boys and two girls, mean age 4.5 years, were admitted for nonspecific respiratory signs. Oriented by radiology findings, the diagnosis of pleuropulmonary blastoma was confirmed at pathology examination of a pneumonectomy specimen. Three of the children were given postoperative adjuvant chemotherapy. There were three deaths and one child,vas lost to follow-up. We discuss the clinical features of pleuropulmonary blastoma. No optimal treatment has been defined for this often fatal tumor.
引用
收藏
页码:390 / 394
页数:5
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