Cardiac pathologies and clinical follow-up of patients with Williams syndrome

被引：2

作者：

Sarisoy, Ozlem ^{[1
]}

Ayabakan, Canan ^{[1
]}

Tokel, Kursad ^{[1
]}

Saritas, Bulent ^{[2
]}

Vuran, Can ^{[2
]}

Ozker, Emre ^{[2
]}

Turkoz, Rasa ^{[2
]}

机构：

[1] Baskent Univ, Istanbul Salik Uygulama & Arastirma Merkezi, Pediat Kardiyol Bolumu, TR-34662 Istanbul, Turkey

[2] Baskent Univ, Istanbul Salik Uygulama & Arastirma Merkezi, Kalp & Damar Cerrahisi Bolumu, TR-34662 Istanbul, Turkey

来源：

TURK GOGUS KALP DAMAR CERRAHISI DERGISI-TURKISH JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY | 2013年 / 21卷 / 04期

关键词：

Aortic stenosis; clinical follow-up; pulmonary stenosis; Williams syndrome; SUPRAVALVULAR AORTIC-STENOSIS; BEUREN-SYNDROME; PULMONARY; OUTCOMES; CHILDREN;

D O I：

10.5606/tgkdc.dergisi.2013.7404

中图分类号：

R61 [外科手术学];

学科分类号：

摘要：

Between August 2008 and August 2011, nine patients (3 girls, 6 boys; mean age 19 +/- 29 months) were admitted to our clinic with Williams syndrome. The mean body weight of the patients was 9454 +/- 5880 g. Two patients had supravalvular aortic stenosis (sAS), one had periferal pulmonary stenosis (PPS), one had supravalvular PS (sPS), two had sAS and sPS, and three had sAS and bilateral PPS. Two patients were not operated. Four patients were operated for sAS and PPS, one patient for sAS, valvular and sPS, one patient for PPS and sPS, and one patient for sAS operation. The gradients were decreased and remained unchanged during follow-up.

引用

页码：1027 / 1031

页数：5

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