Perivascular epitheloid cell tumor (PEComa) mimicking retroperitoneal liposarcoma

被引：14

作者：

Wildgruber, Moritz ^{[1
]}

Becker, Karen ^{[2
]}

Feith, Marcus ^{[3
]}

Gaa, Jochen ^{[1
]}

机构：

[1] Tech Univ Munich, Klinikum Rechts Isar, Dept Diagnost & Intervent Radiol, D-81675 Munich, Germany

[2] Tech Univ Munich, Klinikum Rechts Isar, Dept Pathol, D-80290 Munich, Germany

[3] Tech Univ Munich, Klinikum Rechts Isar, Dept Surg, D-80290 Munich, Germany

来源：

WORLD JOURNAL OF SURGICAL ONCOLOGY | 2014年 / 12卷

关键词：

PEComa; Mesenchymal tumor; Liposarcoma; mTOR signaling; OF-THE-LITERATURE; SUGAR TUMOR; NEOPLASM; PANCREAS; FAMILY;

D O I：

10.1186/1477-7819-12-3

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

PEComas are a collection of generally rare tumors, defined by the World Health Organization as 'mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epitheloid cells'. We describe the case of retroperitoneal PEComa with a liposarcoma-like appearance on cross-sectional imaging, but distinctive immunohistochemistry revealing the correct diagnosis.

引用

页数：4

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