Relapsing Wegener's granulomatosis: Successful treatment with cyclosporin-A

被引:17
作者
Georganas, C [1 ]
Ioakimidis, D [1 ]
Iatrou, C [1 ]
Vidalaki, B [1 ]
Iliadou, K [1 ]
Athanassiou, P [1 ]
Kontomerkos, T [1 ]
机构
[1] DIST GEN HOSP ATHENS,DEPT RHEUMATOL,ATHENS,GREECE
关键词
Wegener's granulomatosis; vasculitis; treatment; cyclophosphamide; cyclosporin-A; plasma exchange; immunoglobulin;
D O I
10.1007/BF02230339
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We describe the case of a 32-year-old splenectomised man with severe Wegener's granulomatosis which was refractory to conventional treatment with oral cyclophosphamide and prednisolone. Remission was temporarily induced only with plasma exchange or IV immunoglobulin. Because of frequent relapses of the disease and cyclophosphamide side effects, he was started on treatment with cyclosporin-ii and a long lasting remission was achieved.
引用
收藏
页码:189 / 192
页数:4
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