Prednisolone-responsive primary sclerosing cholangitis with autoimmune hemolytic anemia: a case report and review of the literature

被引：6

作者：

Kawaguchi, Toshihiro ^{[1
]}

Arinaga-Hino, Teruko ^{[1
]}

Morishige, Satoshi ^{[2
]}

Mizuochi, Shinji ^{[3
]}

Abe, Mitsuhiko ^{[4
]}

Kunitake, Kazuya ^{[1
]}

Sano, Tomoya ^{[1
]}

Amano, Keisuke ^{[1
]}

Kuwahara, Reiichiro ^{[1
]}

Ide, Tatsuya ^{[1
]}

Nagafuji, Koji ^{[2
]}

Torimura, Takuji ^{[1
]}

机构：

[1] Kurume Univ, Sch Med, Dept Med, Div Gastroenterol, 67 Asahi Machi, Kurume, Fukuoka 8300011, Japan

[2] Kurume Univ, Sch Med, Dept Med, Div Hematol & Oncol, Kurume, Fukuoka, Japan

[3] Kurume Univ, Sch Med, Dept Pathol, Kurume, Fukuoka, Japan

[4] Nishinihon Hosp, Dept Gastroenterol, Kumamoto, Japan

来源：

CLINICAL JOURNAL OF GASTROENTEROLOGY | 2021年 / 14卷 / 01期

关键词：

Primary sclerosing cholangitis; Autoimmune hemolytic anemia; Prednisolone;

D O I：

10.1007/s12328-020-01256-8

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

We report a case of primary sclerosing cholangitis (PSC) with autoimmune hemolytic anemia (AIHA). A 47-year-old woman was diagnosed with PSC. One year later, she was admitted to our hospital for jaundice and fatigue. Magnetic resonance cholangiopancreatography (MRCP) showed worsening of the biliary stricture, and rapidly progressive anemia developed simultaneously. Based on the various laboratory findings, she was diagnosed with AIHA. The administration of prednisolone improved not only the anemia but also the biliary stricture. This case is impactful, as there are few case reports of PSC with AIHA. In addition, we were able to observe the changes in imaging findings using MRCP over time.

引用

页码：330 / 335

页数：6

共 22 条

[1]

Bajpai Meenu, 2016, Immunohematology, V32, P104

[2]

BAKER SS, 1991, NEW ENGL J MED, V324, P180

[3] British Society of Gastroenterology and UK-PSC guidelines for the diagnosis and management of primary sclerosing cholangitis [J].