Protein C and protein S deficiency presenting as Budd-Chiari syndrome

被引：3
|
作者：
Uvaraj, Periasamy [1 ]
Rathisharmila, Ramar [1 ]
Ilamaran, Veerappan [1 ]
机构：
[1] Melmaruvathur Adhiparasakthi Inst Med Sci & Res, Dept Paediat, Melmaruvathur 603319, Tamil Nadu, India
来源：
BLOOD COAGULATION & FIBRINOLYSIS | 2013年 / 24卷 / 06期
关键词：
Budd-Chiari syndrome; protein C; protein S; PORTAL-VEIN THROMBOSIS; DEFECTS;
D O I：
10.1097/MBC.0b013e3283609972
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Protein C and S are vitamin K-dependent natural anticoagulants. They play a major role in hemostasis by degrading the activated factor V and factor VIII. Deficiencies of protein C and protein S are associated with increased risk of thrombotic events. The combined occurrence of protein C and S deficiency has been rarely reported. We report a 6-year-old boy with Budd-Chiari syndrome due to combined protein C and protein S deficiency. He was managed with low molecular weight heparin and discharged on long-term warfarin therapy.
引用
收藏
页码：652 / 654
页数：3
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