共 41 条
SOLELY LUNG-INVOLVED IGG4-RELATED DISEASE: A CASE REPORT AND REVIEW OF THE LITERATURE
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作者:

Zhang, Xiao-Qin
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机构:
Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China

Chen, Guo-Ping
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Zhejiang Univ, Affiliated Hosp 1, Dept Endocrinol, Coll Med, Hangzhou 310003, Zhejiang, Peoples R China Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China

Wu, Sheng-Chang
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Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China

Yu, Sa
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Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China

Wang, Hong
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Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China

Chen, Xuan-Yi
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Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China

Ren, Zhuo-Chao
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机构:
Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China
机构:
[1] Zhejiang Prov Peoples Hosp, Dept Respirol, Hangzhou 310014, Zhejiang, Peoples R China
[2] Zhejiang Univ, Affiliated Hosp 1, Dept Endocrinol, Coll Med, Hangzhou 310003, Zhejiang, Peoples R China
关键词:
IgG4-related disease;
immunoglobulin G4;
lung;
IGG4-POSITIVE PLASMA-CELLS;
SERUM IGG4 LEVELS;
AUTOIMMUNE PANCREATITIS;
SYSTEMIC-DISEASE;
INFLAMMATORY PSEUDOTUMOR;
SCLEROSING PANCREATITIS;
ORGANIZING PNEUMONIA;
PULMONARY-DISEASE;
PATIENT;
CANCER;
D O I:
暂无
中图分类号:
R56 [呼吸系及胸部疾病];
学科分类号:
摘要:
By analyzing the clinical data of 1 case of IgG4-related lung disease( IgG4-RLD) and the review of literature, the author investigated the clinical characteristics of IgG4-RLD. IgG4-RLD is a rare disease characterized by significant elevation of serum IgG4 and infiltration of a large number of IgG4+ plasma cells. The clinical manifestations of the disease were nonspecific, and the imaging features were mixed with several types. The disease can only be involved in the lung, but also multiple organ involvement. Solely lung-involved IgG4-RD is not only extremely rare but also easily misdiagnosed as tuberculosis, lung cancer, lymphoma and other common pulmonary diseases. Histopathological examination is the key to the diagnosis of the disease. Corticosteroids are the first choice of treatment, and the overall prognosis is good.
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页码:398 / 406
页数:9
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