Gastroduodenal intussusception due to Peutz-Jeghers Syndrome in infancy

被引：10

作者：

Boseto, F ^{[1
]}

Shi, E ^{[1
]}

Mitchell, J ^{[1
]}

Preddy, J ^{[1
]}

Adams, S ^{[1
]}

机构：

[1] Prince Wales Hosp, Dept Surg, Randwick, NSW 2031, Australia

来源：

PEDIATRIC SURGERY INTERNATIONAL | 2002年 / 18卷 / 2-3期

关键词：

Peutz-Jeghers syndrome; gastric-outlet obstruction; gastroduodenal intussusception;

D O I：

10.1007/s003830100693

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

A case of Peutz-Jeghers Syndrome (PJS) presenting in infancy with gastric-outlet obstruction is described. PJS may become symptomatic at any age and should be suspected when there are obstructive symptoms or crastrointestinal blood loss in a baby with a positive family history. Contrast studies and endoscopy are useful in diagnosis and surveillance. Treatment requires a combination of endoscopy and laparotomy laparoscopy. Because of the reported cancer risk, we recommend surveillance from the age of diagnosis.

引用

页码：178 / 180

页数：3

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