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Pulmonary disease severity in men with ΔF508 cystic fibrosis and residual chloride secretion (vol 353, pg 984, 1999)
被引:0
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作者
:
Thomas, SR
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0
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Thomas, SR
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:
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LANCET
|
1999年
/ 353卷
/ 9166期
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D O I
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:
R5 [内科学];
学科分类号
:
1002 ;
100201 ;
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页码:1804 / 1804
页数:1
相关论文
共 44 条
[21]
Autosomal dominant polycystic kidney disease (ADPKD) and ΔF508 mutation at the cystic fibrosis transmembrane conductance regulator gene.
Peces, R
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Univ Oviedo, Hosp Cent Asturias, Serv Nefrol, E-33080 Oviedo, Spain
Peces, R
Coto, E
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Univ Oviedo, Hosp Cent Asturias, Serv Nefrol, E-33080 Oviedo, Spain
Coto, E
Gago, E
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Univ Oviedo, Hosp Cent Asturias, Serv Nefrol, E-33080 Oviedo, Spain
Gago, E
Ariza, M
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Univ Oviedo, Hosp Cent Asturias, Serv Nefrol, E-33080 Oviedo, Spain
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Laures, AS
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Univ Oviedo, Hosp Cent Asturias, Serv Nefrol, E-33080 Oviedo, Spain
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Alvarez, J
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Cystic fibrosis transmembrane conductance regulator (CFTR)-mediated residual chloride secretion does not protect against early chronic Pseudomonas aeruginosa infection in F508del homozygous cystic fibrosis patients
Derichs, N
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Hannover Med Sch, Dept Pediat, D-30623 Hannover, Germany
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Mekus, F
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Hannover Med Sch, Dept Pediat, D-30623 Hannover, Germany
Mekus, F
Bronsveld, I
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Hannover Med Sch, Dept Pediat, D-30623 Hannover, Germany
Bronsveld, I
Bijman, J
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Hannover Med Sch, Dept Pediat, D-30623 Hannover, Germany
Bijman, J
Veeze, HJ
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Hannover Med Sch, Dept Pediat, D-30623 Hannover, Germany
Veeze, HJ
Von der Hardt, H
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Hannover Med Sch, Dept Pediat, D-30623 Hannover, Germany
Von der Hardt, H
Tümmler, B
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Tümmler, B
Ballmann, M
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Hannover Med Sch, Dept Pediat, D-30623 Hannover, Germany
Ballmann, M
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Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)-Mediated Residual Chloride Secretion Does Not Protect against Early Chronic Pseudomonas aeruginosa Infection in F508del Homozygous Cystic Fibrosis Patients
Nico Derichs
论文数:
0
引用数:
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h-index:
0
机构:
Medizinische Hochschule Hannover,Department of Pediatrics and Clinical CF Research Group
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机构:
Medizinische Hochschule Hannover,Department of Pediatrics and Clinical CF Research Group
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0
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h-index:
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Medizinische Hochschule Hannover,Department of Pediatrics and Clinical CF Research Group
Inez Bronsveld
Jan Bijman
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机构:
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Jan Bijman
Henk J Veeze
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Manfred Ballmann
Pediatric Research,
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[24]
TAS2R38 GENOTYPE CORRELATES WITH AGE AND CHRONICITY OF PSEUDOMONAL PULMONARY COLONIZATION IN THE ΔF508 HOMOZYGOUS CYSTIC FIBROSIS POPULATION
Adappa, N. D.
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Univ Penn, Otorhinolaryngol, Philadelphia, PA 19104 USA
Univ Penn, Otorhinolaryngol, Philadelphia, PA 19104 USA
Adappa, N. D.
Cohen, N. A.
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Univ Penn, Otorhinolaryngol, Philadelphia, PA 19104 USA
Univ Penn, Otorhinolaryngol, Philadelphia, PA 19104 USA
Cohen, N. A.
Dorgan, D.
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Univ Penn, Dept Med, Philadelphia, PA 19104 USA
Univ Penn, Otorhinolaryngol, Philadelphia, PA 19104 USA
Dorgan, D.
Frame, D.
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Univ Penn, Dept Med, Philadelphia, PA 19104 USA
Univ Penn, Otorhinolaryngol, Philadelphia, PA 19104 USA
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Brooks, S.
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Univ Penn, Otorhinolaryngol, Philadelphia, PA 19104 USA
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Brooks, S.
Hadjiliadis, D.
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PEDIATRIC PULMONOLOGY,
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An association study on contrasting cystic fibrosis endophenotypes recognizes KRT8 but not KRT18 as a modifier of cystic fibrosis disease severity and CFTR mediated residual chloride secretion
Stanke, Frauke
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Hannover Med Sch, Dept Pediat, D-3000 Hannover, Germany
Hannover Med Sch, Dept Pediat, D-3000 Hannover, Germany
Stanke, Frauke
Hedtfeld, Silke
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Becker, Tim
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Univ Bonn, Inst Med Biometry Informat & Epidemiol, D-5300 Bonn, Germany
Hannover Med Sch, Dept Pediat, D-3000 Hannover, Germany
Becker, Tim
Tuemmler, Burkhard
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BMC MEDICAL GENETICS,
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Phenylglycine and sulfonamide correctors of defective ΔF508 and G551D cystic fibrosis transmembrane conductance regulator chloride-channel gating
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Suen, YF
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Univ Calif San Francisco, Dept Med, San Francisco, CA 94143 USA
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Univ Calif San Francisco, Dept Med, San Francisco, CA 94143 USA
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Dicus, CW
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Univ Calif San Francisco, Dept Med, San Francisco, CA 94143 USA
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Willenbring, D
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Galietta, LJV
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MOLECULAR PHARMACOLOGY,
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Benzimidazolone activators of chloride secretion: Potential therapeutics for cystic fibrosis and chronic obstructive pulmonary disease
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Univ Pittsburgh, Sch Med, Dept Cell Biol & Physiol, Pittsburgh, PA 15261 USA
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Singh, S
Syme, CA
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Univ Pittsburgh, Sch Med, Dept Cell Biol & Physiol, Pittsburgh, PA 15261 USA
Univ Pittsburgh, Sch Med, Dept Cell Biol & Physiol, Pittsburgh, PA 15261 USA
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Singh, AK
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Univ Pittsburgh, Sch Med, Dept Cell Biol & Physiol, Pittsburgh, PA 15261 USA
Univ Pittsburgh, Sch Med, Dept Cell Biol & Physiol, Pittsburgh, PA 15261 USA
Singh, AK
Devor, DC
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Univ Pittsburgh, Sch Med, Dept Cell Biol & Physiol, Pittsburgh, PA 15261 USA
Univ Pittsburgh, Sch Med, Dept Cell Biol & Physiol, Pittsburgh, PA 15261 USA
Devor, DC
Bridges, RJ
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Univ Pittsburgh, Sch Med, Dept Cell Biol & Physiol, Pittsburgh, PA 15261 USA
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LESTER, LA
KRAUT, J
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BILLSTRAND, C
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OBER, C
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PEDIATRICS,
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RETRACTED: Protein kinase CK2, cystic fibrosis transmembrane conductance regulator, and the ΔF508 mutation (Retracted Article. See vol 283, pg 25103, 2008)
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Xu, Zhe
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机构:
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机构:
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机构:
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Johns Hopkins Univ, Sch Med, Dept Biol Chem, Baltimore, MD 21205 USA
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Johns Hopkins Univ, Sch Med, Dept Biol Chem, Baltimore, MD 21205 USA
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Johns Hopkins Univ, Sch Med, Dept Biol Chem, Baltimore, MD 21205 USA
Johns Hopkins Univ, Sch Med, Dept Biol Chem, Baltimore, MD 21205 USA
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