Severe, obstructive biventricular hypertrophy in a patient with Costello syndrome: Clinical impact and management

被引：7

作者：

Limongelli, Giuseppe ^{[1
]}

Pacileo, Giuseppe ^{[1
]}

Digilio, Maria Cristina ^{[2
]}

Calabro', Paolo ^{[1
]}

Di Salvo, Giovanni ^{[1
]}

Rea, Alessandra ^{[1
]}

Miele, Tiziana ^{[1
]}

Frigiola, Alessandro ^{[5
]}

Sarkozy, Anna ^{[4
]}

Dallapiccola, Bruno ^{[4
]}

Marino, Bruno ^{[3
]}

Calabro', Raffaele ^{[1
]}

机构：

[1] Univ Naples 2, Monaldi Hosp, Dept Cardiol, Naples, Italy

[2] Bambino Gesu Pediat Hosp, Rome, Italy

[3] Univ Roma La Sapienza, Dept Pediat, Rome, Italy

[4] Mendel Inst Med Genet & Twin Res, IRCCS CSS, San Giovanni Rotondo & CSS, Rome, Italy

[5] IRCCS Policlin San Donato, Pediat Cardiol & Cardiac Surg Dept, Milan, Italy

来源：

INTERNATIONAL JOURNAL OF CARDIOLOGY | 2008年 / 130卷 / 03期

关键词：

Cardiac hypertrophy; Costello syndrome; Management;

D O I：

10.1016/j.ijcard.2007.06.107

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

We report a severe, biventricular obstructive cardiomyopathy in a young female with Costello syndrome, who underwent a right ventricular myectomy for symptoms relief. We discuss potential clinical implications and management of severe hypertrophy in Costello syndrome. (C) 2007 Published by Elsevier Ireland Ltd.

引用

页码：E108 / E110

页数：3

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