Gorham-Stout Disease and Cerebrospinal Fluid Otorrhea

被引:17
作者
Hernandez-Marques, Carmen [1 ]
Serrano Gonzalez, Ana [2 ]
Cordobes Ortega, Francisco [3 ]
Alvarez-Coca, Javier [4 ]
Sirvent Cerda, Sara [5 ]
Carceller Lechon, Fernando [1 ]
Azorin Cuadrillero, Daniel [6 ]
机构
[1] Hosp Infantil Univ Nino Jesus, Dept Pediat Hematol Oncol, ES-28009 Madrid, Spain
[2] Hosp Infantil Univ Nino Jesus, Pediat Intens Care Unit, ES-28009 Madrid, Spain
[3] Hosp Infantil Univ Nino Jesus, Dept Neurosurg, ES-28009 Madrid, Spain
[4] Hosp Infantil Univ Nino Jesus, Dept Pediat, ES-28009 Madrid, Spain
[5] Hosp Infantil Univ Nino Jesus, Dept Radiol, ES-28009 Madrid, Spain
[6] Hosp Infantil Univ Nino Jesus, Dept Pathol, ES-28009 Madrid, Spain
关键词
Gorham-Stout disease; Temporal bone; Cerebrospinal fluid otorrhea; MASSIVE OSTEOLYSIS; DISAPPEARING BONE; CERVICAL-SPINE;
D O I
10.1159/000336877
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Objective and Importance: Gorham-Stout disease is a rare entity characterized by vascular proliferation causing local destruction of bone tissue. Owing to its low incidence and variable clinical presentation, the diagnosis requires a high degree of awareness by the clinician. Clinical Presentation: We present the case of a 2-year-old boy diagnosed of Gorham-Stout syndrome with involvement of the temporal bone and secondary cerebrospinal fluid (CSF) leakage. Intervention: Because of the CSF leakage, the patient required two surgical interventions. The second intervention included mastectomy and placement of a patch and a lumbar drainage device during 50 days, after which the leakage ceased. Conclusion: Gorham-Stout disease is a rare condition that can affect the skull base and even present with CSF leakage. Copyright (C) 2012 S. Karger AG, Basel
引用
收藏
页码:299 / 302
页数:4
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