Biliary atresia: East versus west

被引:42
作者
Chung, Patrick Ho Yu [1 ]
Zheng, Shan [2 ]
Tam, Paul Kwong Hang [1 ]
机构
[1] Univ Hong Kong, Li Ka Shing Fac Med, Div Paediat Surg, Dept Surg, Hong Kong, Peoples R China
[2] Fudan Univ, Childrens Hosp, Dept Pediat Surg, Shanghai Key Lab Birth Defect, Shanghai, Peoples R China
关键词
Biliary atresia; Kasai portoenterostomy; Liver transplant; Biliary atresia splenic malformation syndrome; LAPAROSCOPIC KASAI PORTOENTEROSTOMY; PEDIATRIC LIVER-TRANSPLANTATION; STOOL COLOR CARD; OUTCOMES; CENTRALIZATION;
D O I
10.1016/j.sempedsurg.2020.150950
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Biliary atresia (BA) is a common cause of surgical jaundice during the neonatal period. It is currently considered as a spectrum of diseases with a common final pathology characterized by obliteration of the extrahepatic biliary tract and the absence of normally branching intrahepatic ducts. Though it is a global disease that can be found in all ethnicities there are some clear differences between BA arising in the East and the West. This is likely to be related to different genetic, environmental and cultural factors. BA is more frequently found in Far Eastern infants (both Chinese and Japanese) though the syndromic associations are much less common. Many Eastern countries have national screening programmes not seen in the West possibly due to debate over its cost effectiveness in countries where incidence is low. Kasai portoenterostomy (KPE) is considered as the primary treatment of BA but its outcome still remains unsatisfactory across the region. Given the complexity of BA, it is unlikely that strategic advances could be made by the sole effort of individual countries and we believe that collaboration between the East and West is the way forward. (C) 2020 Elsevier Inc. All rights reserved.
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页数:6
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