Tetralogy of Fallot: Everything you wanted to know but were afraid to ask

被引:30
作者
Wise-Faberowski, Lisa [1 ]
Asija, Ritu [2 ]
McElhinney, Doff B. [3 ]
机构
[1] Stanford Univ, Dept Anesthesiol, Palo Alto, CA 94304 USA
[2] Stanford Univ, Dept Pediat, Palo Alto, CA 94304 USA
[3] Stanford Univ, Dept Surg, Palo Alto, CA 94304 USA
关键词
cardiac; children; congenital heart disease; infants; neonates; surgery; CONGENITAL HEART-DISEASE; JUNCTIONAL ECTOPIC TACHYCARDIA; VENTRICULAR SEPTAL-DEFECT; PULMONARY-ATRESIA; 22Q11.2; DELETION; ABNORMALITIES; ASSOCIATION; PREVALENCE; MUTATIONS; CHILDREN;
D O I
10.1111/pan.13569
中图分类号
R614 [麻醉学];
学科分类号
100217 ;
摘要
Tetralogy of Fallot (TOF) has four anatomic features: right ventricular hypertrophy (RVH), ventriculoseptal defect (VSD), overriding aorta and right ventricular outflow tract obstruction (RVOT) with an occurrence of 3.9 /10,000 births. The pathophysiologic effects in TOF are largely determined by the degree of RVOT and not the VSD. Intra-operative anesthetic management is also dependent on the degree of RVOT obstruction and influenced by the extent of surgical RVOT repair.
引用
收藏
页码:475 / 482
页数:8
相关论文
共 42 条
[1]   Junctional ectopic tachycardia after surgery for congenital heart disease in children [J].
Andreasen, J. B. ;
Johnsen, S. P. ;
Ravn, H. B. .
INTENSIVE CARE MEDICINE, 2008, 34 (05) :895-902
[2]   Jagged1 (JAG1) Mutations in Patients with Tetralogy of Fallot or Pulmonic Stenosis [J].
Bauer, Robert C. ;
Laney, Ayanna O. ;
Smith, Rosemarie ;
Geffen, Jennifer ;
Morrissette, Jennifer J. D. ;
Woyciechowski, Stacy ;
Garbarini, Jennifer ;
Loomes, Kathleen M. ;
Krantz, Ian D. ;
Urban, Zsolt ;
Gelb, Bruce D. ;
Goldmuntz, Elizabeth ;
Spinner, Nancy B. .
HUMAN MUTATION, 2010, 31 (05) :594-601
[3]   Programmatic Approach to Management of Tetralogy of Fallot With Major Aortopulmonary Collateral Arteries A 15-Year Experience With 458 Patients [J].
Bauser-Heaton, Holly ;
Borquez, Alejandro ;
Han, Brian ;
Ladd, Michael ;
Asija, Ritu ;
Downey, Laura ;
Koth, Andrew ;
Algaze, Claudia A. ;
Wise-Faberowski, Lisa ;
Perry, Stanton B. ;
Shin, Andrew ;
Peng, Lynn F. ;
Hanley, Frank L. ;
McElhinney, Doff B. .
CIRCULATION-CARDIOVASCULAR INTERVENTIONS, 2017, 10 (04)
[4]  
Breitbart R., 2006, NADAS PEDIAT CARDIOL, P559
[5]  
Brizard Christian P, 2009, Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu, P139, DOI 10.1053/j.pcsu.2009.01.016
[6]  
Chen Q, 2014, EUR J CARDIO-THORAC, V46, P297
[7]   Pulmonary atresia with ventricular septal defects and major aortopulmonary collateral arteries: Unifocalization brings no long-term benefits [J].
d'Udekem, Y ;
Alphonso, N ;
Norgaard, MA ;
Cochrane, AD ;
Grigg, LE ;
Wilkinson, JL ;
Brizard, CP .
JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY, 2005, 130 (06) :1496-1502
[8]   DISTRIBUTION AND ANOMALIES OF CORONARY-ARTERIES IN TETRALOGY OF FALLOT [J].
DABIZZI, RP ;
CAPRIOLI, G ;
AIAZZI, L ;
CASTELLI, C ;
BALDRIGHI, G ;
PARENZAN, L ;
BALDRIGHI, V .
CIRCULATION, 1980, 61 (01) :95-102
[9]   CONGENITAL HEART-DISEASE - PREVALENCE AT LIVEBIRTH - THE BALTIMORE WASHINGTON INFANT STUDY [J].
FERENCZ, C ;
RUBIN, JD ;
MCCARTER, RJ ;
BRENNER, JI ;
NEILL, CA ;
PERRY, LW ;
HEPNER, SI ;
DOWNING, JW .
AMERICAN JOURNAL OF EPIDEMIOLOGY, 1985, 121 (01) :31-36
[10]  
Freeman SB, 1998, AM J MED GENET, V80, P213, DOI 10.1002/(SICI)1096-8628(19981116)80:3<213::AID-AJMG6>3.0.CO