Korean Guidelines for Diagnosis and Management of Interstitial Lung Diseases: Part 2. Idiopathic Pulmonary Fibrosis

被引：33

作者：

Lee, Sang Hoon ^{[1
]}

Yeo, Yoomi ^{[2
]}

Kim, Tae-Hyung ^{[2
]}

Lee, Hong Lyeol ^{[3
]}

Lee, Jin Hwa ^{[4
]}

Park, Yong Bum ^{[5
]}

Park, Jong Sun ^{[6
]}

Kim, Yee Hyung ^{[7
]}

Song, Jin Woo ^{[8
]}

Jhun, Byung Woo ^{[9
]}

Kim, Hyun Jung ^{[10
]}

Park, Jinkyeong ^{[9
]}

Uh, Soo-Taek ^{[11
]}

Kim, Young Whan ^{[12
]}

Kim, Dong Soon ^{[8
]}

Park, Moo Suk ^{[1
]}

机构：

[1] Yonsei Univ, Severance Hosp, Inst Chest Dis, Dept Internal Med,Coll Med,Div Pulmonol, 50-1 Yonsei Ro, Seoul 03722, South Korea

[2] Hanyang Univ, Guri Hosp, Div Pulm & Crit Care Med, Coll Med, Guri, South Korea

[3] Inha Univ, Inha Univ Hosp, Dept Internal Med, Div Pulm & Crit Care Med,Coll Med, Incheon, South Korea

[4] Ewha Womans Univ, Dept Internal Med, Div Pulm & Crit Care Med, Coll Med, Seoul, South Korea

[5] Hallym Univ, Coll Med, Dept Internal Med, Kangdong Sacred Heart Hosp,Lung Res Inst, Seoul, South Korea

[6] Seoul Natl Univ, Bundang Hosp, Dept Internal Med, Div Pulm & Crit Care Med,Coll Med, Seongnam, South Korea

[7] Kyung Hee Univ Hosp Gangdong, Div Pulm & Crit Care Med, Seoul, South Korea

[8] Univ Ulsan, Asan Med Ctr, Dept Pulm & Crit Care Med, Coll Med, Seoul, South Korea

[9] Sungkyunkwan Univ, Samsung Med Ctr, Div Pulm & Crit Care Med, Sch Med, Seoul, South Korea

[10] Keimyung Univ, Dept Internal Med, Sch Med, Daegu, South Korea

[11] Soonchunhyang Univ, Dept Internal Med, Seoul Hosp, Seoul, South Korea

[12] Seoul Natl Univ Hosp, Dept Internal Med, Div Pulm & Crit Care Med, Seoul, South Korea

来源：

TUBERCULOSIS AND RESPIRATORY DISEASES | 2019年 / 82卷 / 02期

关键词：

Idiopathic Pulmonary Fibrosis; Diagnosis; Disease Management; Korea; ENDOPLASMIC-RETICULUM STRESS; ACID GASTROESOPHAGEAL-REFLUX; FORCED VITAL CAPACITY; ACUTE EXACERBATION; PREDICTING SURVIVAL; EPITHELIAL-CELLS; GENE-EXPRESSION; HIGH PREVALENCE; SCORING SYSTEM; CT FINDINGS;

D O I：

10.4046/trd.2018.0091

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive fibrosing interstitial pneumonia, which presents with a progressive worsening dyspnea, and thus a poor outcome. The members of the Korean Academy of Tuberculosis and Respiratory Diseases as well as the participating members of the Korea Interstitial Lung Disease Study Group drafted this clinical practice guideline for IPF management. This guideline includes a wide range of topics, including the epidemiology, pathogenesis, risk factors, clinical features, diagnosis, treatment, prognosis, and acute exacerbation of IPF in Korea Additionally, we suggested the PICO for the use of pirfenidone and nintendanib and for lung transplantation for the treatment of patients with IPF through a systemic literature review using experts help in conducting a meta-analysis. We recommend this guideline to physicians, other health care professionals, and government personnel in Korea, to facilitate the treatment of patients with IPF.

引用

页码：102 / 117

页数：16

共 115 条

[1] CT findings during phase of accelerated deterioration in patients with idiopathic pulmonary fibrosis [J].