Somatostatinoma of the First Jejunal Loop in a Patient with Neurofibromatosis Von Recklinghausen and Bilateral Pheochromocytoma

被引：2

作者：

Constantinoiu, Silvia ^{[1
]}

Constantin, Adrian ^{[1
]}

Predescu, Dragos ^{[1
]}

Iosif, Cristina ^{[2
]}

Hoara, Petre ^{[1
]}

Achim, Florin ^{[1
]}

Surugiu, Paul ^{[1
]}

Bacanu, Florin ^{[3
]}

Cociu, Luminita ^{[4
]}

机构：

[1] Univ Med & Pharm Carol Davila, Gen & Esophageal Surg Clin, St Marys Hosp Bucharest, Bucharest 011172, Romania

[2] Univ Med & Pharm Carol Davila, Dept Pathol, St Marys Hosp Bucharest, Bucharest 011172, Romania

[3] Univ Med & Pharm Carol Davila, Dept Oncol, St Marys Hosp Bucharest, Bucharest 011172, Romania

[4] Univ Med & Pharm Carol Davila, Intens Care Unit, St Marys Hosp Bucharest, Bucharest 011172, Romania

来源：

HEPATO-GASTROENTEROLOGY | 2012年 / 59卷 / 118期

关键词：

Jejunal somatostatinoma; Neurofibromatosis; Von Recklinghausen; Pheochromocytoma; DUODENAL SOMATOSTATINOMA; TUMORS; DISEASE; MANAGEMENT; SECRETION; PANCREAS; FEATURES;

D O I：

10.5754/hge11571

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

Somatostatinoma is a rare neuroendocrine tumor which especially develops in the pancreas. There are few communicated cases about extra-pancreatic localization, having as a particularity the absence of somatostatin hypersecretion syndrome and frequent association with von Recklinghausen neurofibromatosis. We present the case of a 42-year old patient with Von Recklinghausen neurofibromatosis admitted in our clinic with a chronic upper digestive obstruction syndrome. The presence of a first jejunal loop somatostatinoma was an intraoperative surprising diagnosis that imposed jejunal resection and association of complementary specific treatment. Despite the therapeutic correct management, the status of the patient deteriorated very fast, confirming the aggressiveness of this neoplasia.

引用

页码：1874 / 1878

页数：5

共 19 条

[1] JEJUNAL ENDOCRINE TUMOR COMPOSED OF SOMATOSTATIN AND GASTRIN CELLS AND ASSOCIATED WITH DUODENAL-ULCER DISEASE [J].