Acquired angioedema

被引:25
作者
Heymann, WR
机构
[1] Robert Wood Johnson Medical School, UMDNJ, Marlton, NJ 08053
关键词
D O I
10.1016/S0190-9622(97)70250-0
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Acquired angioedema (AAE) is a rare disorder that has been categorized into two forms, AAE-I and AAE-II. AAE-I is associated with other diseases, most commonly B-cell lymphoproliferative disorders. AAE-II is defined by the presence of an autoantibody directed against the C1-inhibitor molecule. Differentiating AAE-I from AAE-II is vital because different therapeutic interventions are required for each type. This review summarizes the clinical aspects, pathophysiology, and management of AAE compared with the types of hereditary angioedema.
引用
收藏
页码:611 / 615
页数:5
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