CTLA-4 Expression in CD4+ T Cells From Patients With LRBA Deficiency and Common Variable Immunodeficiency With No Known Monogenic Disease

被引:12
作者
Azizi, G. [1 ,2 ,3 ]
Jamee, M. [4 ]
Yazdani, R. [2 ]
Bagheri, Y. [5 ,6 ]
Fayyaz, F. [4 ]
Jadidi-Niaragh, F. [7 ,8 ]
Abolhassani, H. [2 ,9 ]
Aghamohammadi, A. [2 ]
机构
[1] Alborz Univ Med Sci, Non Communicable Dis Res Ctr, Karaj, Iran
[2] Univ Tehran Med Sci, Res Ctr Immunodeficiencies, Childrens Med Ctr, Tehran, Iran
[3] USERN, Primary Immunodeficiency Dis Network PIDNet, Tehran, Iran
[4] Alborz Univ Med Sci, Student Res Comm, Alborz, Iran
[5] Golestan Univ Med Sci, 5 Azar Hosp, Clin Res Dev Unit CRDU, Gorgan, Golestan, Iran
[6] Iran Univ Med Sci, Dept Allergy & Clin Immunol, Tehran, Iran
[7] Tabriz Univ Med Sci, Immunol Res Ctr, Tabriz, Iran
[8] Tabriz Univ Med Sci, Sch Med, Dept Immunol, Tabriz, Iran
[9] Karolinska Inst, Karolinska Univ Hosp Huddinge, Div Clin Immunol, Dept Lab Med, Stockholm, Sweden
关键词
Common variable immunodeficiency; LRBA deficiency; CTLA-4; IMMUNE DYSREGULATION;
D O I
10.18176/jiaci.0302
中图分类号
R392 [医学免疫学];
学科分类号
100102 ;
摘要
[No abstract available]
引用
收藏
页码:422 / +
页数:3
相关论文
共 10 条
[1]   Two Faces of LRBA Deficiency in Siblings: Hypogammaglobulinemia and Normal Immunoglobulin Levels [J].
Azizi, G. ;
Abolhassani, H. ;
Habibi, S. ;
Rahamooz, T. ;
Mohammadi, H. ;
Jafarnezhad-Ansariha, F. ;
Mortazavi-jahromi, S. S. ;
Yazdani, R. ;
Aghamohammadi, A. .
JOURNAL OF INVESTIGATIONAL ALLERGOLOGY AND CLINICAL IMMUNOLOGY, 2018, 28 (01) :48-50
[2]   T-Cell Abnormalities in Common Variable Immunodeficiency [J].
Azizi, G. ;
Rezaei, N. ;
Kiaee, F. ;
Tavakolinia, N. ;
Yazdani, R. ;
Mirshafiey, A. ;
Aghamohammadi, A. .
JOURNAL OF INVESTIGATIONAL ALLERGOLOGY AND CLINICAL IMMUNOLOGY, 2016, 26 (04) :233-243
[3]  
Azizi G, 2018, J INVESTIG ALLERGOL
[4]   Clinical, immunologic, molecular analyses and outcomes of iranian patients with LRBA deficiency: A longitudinal study [J].
Azizi, Gholamreza ;
Abolhassani, Hassan ;
Mahdaviani, Seyed Alireza ;
Chavoshzadeh, Zahra ;
Eshghi, Peyman ;
Yazdani, Reza ;
Kiaee, Fatemeh ;
Shaghaghi, Mohammadreza ;
Mohammadi, Javad ;
Rezaei, Nima ;
Hammarstrom, Lennart ;
Aghamohammadi, Asghar .
PEDIATRIC ALLERGY AND IMMUNOLOGY, 2017, 28 (05) :478-484
[5]   Autoimnriunity in Primary Antibody Deficiencies [J].
Azizi, Gholamreza ;
Ahmadi, Moslem ;
Abolhassani, Hassan ;
Yazdani, Reza ;
Mohammadi, Hamed ;
Mirshafiey, Abbas ;
Rezaei, Nima ;
Aghamohammadi, Asghar .
INTERNATIONAL ARCHIVES OF ALLERGY AND IMMUNOLOGY, 2016, 171 (3-4) :180-193
[6]   Cellular and molecular mechanisms of immune dysregulation and autoimmunity [J].
Azizi, Gholamreza ;
Pouyani, Mohsen Rastegar ;
Abolhassani, Hassan ;
Sharifi, Laleh ;
Dizaji, Majid Zaki ;
Mohammadi, Javad ;
Mirshafiey, Abbas ;
Aghamohammadi, Asghar .
CELLULAR IMMUNOLOGY, 2016, 310 :14-26
[7]   Genes associated with common variable immunodeficiency: one diagnosis to rule them all? [J].
Bogaert, Delfien J. A. ;
Dullaers, Melissa ;
Lambrecht, Bart N. ;
Vermaelen, Karim Y. ;
De Baere, Elfride ;
Haerynck, Filomeen .
JOURNAL OF MEDICAL GENETICS, 2016, 53 (09) :575-590
[8]   Identifying functional defects in patients with immune dysregulation due to LRBA and CTLA-4 mutations [J].
Hou, Tie Zheng ;
Verma, Nisha ;
Wanders, Jennifer ;
Kennedy, Alan ;
Soskic, Blagoje ;
Janman, Daniel ;
Halliday, Neil ;
Rowshanravan, Behzad ;
Worth, Austen ;
Qasim, Waseem ;
Baxendale, Helen ;
Stauss, Hans ;
Seneviratne, Suranjith ;
Neth, Olaf ;
Olbrich, Peter ;
Hambleton, Sophie ;
Arkwright, Peter D. ;
Burns, Siobhan O. ;
Walker, Lucy S. K. ;
Sansom, David M. .
BLOOD, 2017, 129 (11) :1458-1468
[9]   Patients with LRBA deficiency show CTLA4 loss and immune dysregulation responsive to abatacept therapy [J].
Lo, Bernice ;
Zhang, Kejian ;
Lu, Wei ;
Zheng, Lixin ;
Zhang, Qian ;
Kanellopoulou, Chrysi ;
Zhang, Yu ;
Liu, Zhiduo ;
Fritz, Jill M. ;
Marsh, Rebecca ;
Husami, Ammar ;
Kissell, Diane ;
Nortman, Shannon ;
Chaturvedi, Vijaya ;
Haines, Hilary ;
Young, Lisa R. ;
Mo, Jun ;
Filipovich, Alexandra H. ;
Bleesing, Jack J. ;
Mustillo, Peter ;
Stephens, Michael ;
Rueda, Cesar M. ;
Chougnet, Claire A. ;
Hoebe, Kasper ;
McElwee, Joshua ;
Hughes, Jason D. ;
Karakoc-Aydiner, Elif ;
Matthews, Helen F. ;
Price, Susan ;
Su, Helen C. ;
Rao, V. Koneti ;
Lenardo, Michael J. ;
Jordan, Michael B. .
SCIENCE, 2015, 349 (6246) :436-440
[10]   Asthma and Allergic Diseases in a Selected Group of Patients With Common Variable Immunodeficiency [J].
Yazdani, R. ;
Heydari, A. ;
Azizi, G. ;
Abolhassani, H. ;
Aghamohammadi, A. .
JOURNAL OF INVESTIGATIONAL ALLERGOLOGY AND CLINICAL IMMUNOLOGY, 2016, 26 (03) :209-211