Proteus Syndrome High-resolution CT and CT Pulmonary Densitovolumetry Findings

被引:14
|
作者
Irion, Klaus L. [1 ,2 ,3 ]
Hocchegger, Bruno [4 ,5 ]
Marchiori, Edson [4 ,5 ]
Holemans, John A. [1 ,2 ,3 ]
Smith, Rupert A. [6 ]
Raja, Ramesh C. [6 ]
Singanayagam, Selvadurai [6 ]
机构
[1] Liverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
[2] Royal Liverpool Univ Hosp, Liverpool, Merseyside, England
[3] Postgrad Program Resp Sci UFRGS, Porto Alegre, RS, Brazil
[4] UFRJ, Postgrad Program Radiol, Rio De Janeiro, Brazil
[5] Univ Fed Fluminense, Niteroi, RJ, Brazil
[6] Pennine Acute Hosp NHS Trust, Great Manchester, Brazil
关键词
Proteus syndrome; high-resolution computed tomography; chest; quantitative computed tomography; DIAGNOSTIC-CRITERIA; COMPUTED DENSITY; MANIFESTATIONS; MORPHOMETRY; EMPHYSEMA; DEATH;
D O I
10.1097/RTI.0b013e31818b20cd
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Cystic transformation of the lungs in Proteus syndrome is considered an important manifestation of this disease. We describe a case of an 11-year-old girl with a diagnosis of Proteus syndrome with lung involvement. Low-dose multidetector computed tomography (CT) revealed extensive diffuse cystic lung disease wit 1 left long predominance. affecting mostly the lower lung zones. The cystic lesions had various sizes and variable wall thickness. Postprocessing using CT histogram densitometric volumetry software (CT densitovolumetry), using the threshold -950 Houndsfield units (HU) for quantifying emphysema, revelled that 31%. of her total lung volume was composed of areas with CT. attenuation values below -950 HU.
引用
收藏
页码:45 / 48
页数:4
相关论文
共 50 条
  • [41] Gaussian Mixture Modeling for Statistical Analysis of Features of High-Resolution CT Images of Diffuse Pulmonary Diseases
    Almeida, Eliana
    Rangayyan, Rangaraj M.
    Azevedo-Marques, Paulo M.
    2015 IEEE INTERNATIONAL SYMPOSIUM ON MEDICAL MEASUREMENTS AND APPLICATIONS (MEMEA) PROCEEDINGS, 2015, : 1 - 5
  • [42] Typical and atypical pattern of pulmonary sarcoidosis at high-resolution CT: relation to clinical evolution and therapeutic procedures
    Polverosi, Roberta
    Russo, Rosangela
    Coran, Alessandro
    Battista, Anna
    Agostini, Carlo
    Pomerri, Fabio
    Giraudo, Chiara
    RADIOLOGIA MEDICA, 2014, 119 (06): : 384 - 392
  • [43] Solitary pulmonary nodules - Optimal slice thickness of high-resolution CT in differentiating malignant from benign
    Iwano, S
    Makino, N
    Ikeda, M
    Itoh, S
    Tadokoro, M
    Satake, H
    Ishigaki, T
    CLINICAL IMAGING, 2004, 28 (05) : 322 - 328
  • [44] REGIONAL DISTRIBUTION OF EMPHYSEMA - CORRELATION OF HIGH-RESOLUTION CT WITH PULMONARY-FUNCTION TESTS IN UNSELECTED SMOKERS
    GURNEY, JW
    JONES, KK
    ROBBINS, RA
    GOSSMAN, GL
    NELSON, KJ
    DAUGHTON, D
    SPURZEM, JR
    RENNARD, SI
    RADIOLOGY, 1992, 183 (02) : 457 - 463
  • [45] Pulmonary paracoccidioidomycosis: A case report with high-resolution computed tomography findings
    Armas, M.
    Ruivo, C.
    Alves, R.
    Goncalves, M.
    Teixeira, L.
    REVISTA PORTUGUESA DE PNEUMOLOGIA, 2012, 18 (04) : 190 - 193
  • [46] Comparison between conventional interrupted high-resolution CT and volume multidetector CT acquisition in the assessment of bronchiectasis
    Hill, L. E.
    Ritchie, G.
    Wightman, A. J.
    Hill, A. T.
    Murchison, J. T.
    BRITISH JOURNAL OF RADIOLOGY, 2010, 83 (985) : 67 - 70
  • [47] High-resolution CT in smoking-related interstitial lung diseases
    Carlicchi, E.
    Caminati, A.
    Fughelli, P.
    Pelosi, G.
    Harari, S.
    Zompatori, M.
    INTERNATIONAL JOURNAL OF TUBERCULOSIS AND LUNG DISEASE, 2021, 25 (02) : 106 - +
  • [48] Micronodular lung disease on high-resolution CT: patterns and differential diagnosis
    Kim, J.
    Dabiri, B.
    Hammer, M. M.
    CLINICAL RADIOLOGY, 2021, 76 (06) : 399 - 406
  • [49] A HIGH-RESOLUTION XRII-BASED QUANTITATIVE VOLUME CT SCANNER
    HOLDSWORTH, DW
    DRANGOVA, M
    FENSTER, A
    MEDICAL PHYSICS, 1993, 20 (02) : 449 - 462
  • [50] Nonspecific interstitial pneumonia:: Variable appearance at high-resolution chest CT
    Hartman, TE
    Swensen, SJ
    Hansell, DM
    Colby, TV
    Myers, JL
    Tazelaar, HD
    Nicholson, AG
    Wells, AU
    Rau, JH
    Mu'adhdhin, DE
    du Bois, RM
    Müller, NL
    RADIOLOGY, 2000, 217 (03) : 701 - 705