Proteus Syndrome High-resolution CT and CT Pulmonary Densitovolumetry Findings
被引:14
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作者:
Irion, Klaus L.
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机构:
Liverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Royal Liverpool Univ Hosp, Liverpool, Merseyside, England
Postgrad Program Resp Sci UFRGS, Porto Alegre, RS, BrazilLiverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Irion, Klaus L.
[1
,2
,3
]
Hocchegger, Bruno
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UFRJ, Postgrad Program Radiol, Rio De Janeiro, Brazil
Univ Fed Fluminense, Niteroi, RJ, BrazilLiverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Hocchegger, Bruno
[4
,5
]
Marchiori, Edson
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机构:
UFRJ, Postgrad Program Radiol, Rio De Janeiro, Brazil
Univ Fed Fluminense, Niteroi, RJ, BrazilLiverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Marchiori, Edson
[4
,5
]
Holemans, John A.
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机构:
Liverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Royal Liverpool Univ Hosp, Liverpool, Merseyside, England
Postgrad Program Resp Sci UFRGS, Porto Alegre, RS, BrazilLiverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Holemans, John A.
[1
,2
,3
]
Smith, Rupert A.
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机构:
Pennine Acute Hosp NHS Trust, Great Manchester, BrazilLiverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Smith, Rupert A.
[6
]
Raja, Ramesh C.
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机构:
Pennine Acute Hosp NHS Trust, Great Manchester, BrazilLiverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Raja, Ramesh C.
[6
]
Singanayagam, Selvadurai
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Pennine Acute Hosp NHS Trust, Great Manchester, BrazilLiverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
Singanayagam, Selvadurai
[6
]
机构:
[1] Liverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England
[2] Royal Liverpool Univ Hosp, Liverpool, Merseyside, England
[3] Postgrad Program Resp Sci UFRGS, Porto Alegre, RS, Brazil
[4] UFRJ, Postgrad Program Radiol, Rio De Janeiro, Brazil
[5] Univ Fed Fluminense, Niteroi, RJ, Brazil
[6] Pennine Acute Hosp NHS Trust, Great Manchester, Brazil
Cystic transformation of the lungs in Proteus syndrome is considered an important manifestation of this disease. We describe a case of an 11-year-old girl with a diagnosis of Proteus syndrome with lung involvement. Low-dose multidetector computed tomography (CT) revealed extensive diffuse cystic lung disease wit 1 left long predominance. affecting mostly the lower lung zones. The cystic lesions had various sizes and variable wall thickness. Postprocessing using CT histogram densitometric volumetry software (CT densitovolumetry), using the threshold -950 Houndsfield units (HU) for quantifying emphysema, revelled that 31%. of her total lung volume was composed of areas with CT. attenuation values below -950 HU.
机构:
Complexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, SpainComplexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, Spain
Arango-Diaz, A.
Martinez-de-Alegria-Alonso, A.
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Complexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, SpainComplexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, Spain
Martinez-de-Alegria-Alonso, A.
Baleato-Gonzalez, S.
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Complexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, SpainComplexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, Spain
Baleato-Gonzalez, S.
Garcia-Figueiras, R.
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Complexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, SpainComplexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, Spain
Garcia-Figueiras, R.
Ecenarro-Montiel, A.
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机构:
Complexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, SpainComplexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, Spain
Ecenarro-Montiel, A.
Trujillo-Ariza, M., V
论文数: 0引用数: 0
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机构:
Complexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, SpainComplexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, Spain
Trujillo-Ariza, M., V
Lama-Lopez, A.
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机构:
Complexo Hosp Univ Santiago de Compostela CHUS, Dept Pulmonol, Santiago De Compostela 15706, SpainComplexo Hosp Univ Santiago de Compostela CHUS, Dept Radiol, Rua Choupana S-N, Santiago De Compostela 15706, Spain
机构:
Tampere Univ Hosp, Med Imaging Ctr, Tampere 33521, FinlandTampere Univ Hosp, Med Imaging Ctr, Tampere 33521, Finland
Paakkala, Antti
Jarvenpaa, Ritva
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机构:
Tampere Univ Hosp, Med Imaging Ctr, Tampere 33521, FinlandTampere Univ Hosp, Med Imaging Ctr, Tampere 33521, Finland
Jarvenpaa, Ritva
Makela, Satu
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机构:
Tampere Univ Hosp, Dept Internal Med, Tampere 33521, Finland
Univ Tampere, Sch Med, Tampere 33521, FinlandTampere Univ Hosp, Med Imaging Ctr, Tampere 33521, Finland
Makela, Satu
Huhtala, Heini
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Univ Tampere, Sch Publ Hlth, Tampere 33521, FinlandTampere Univ Hosp, Med Imaging Ctr, Tampere 33521, Finland
Huhtala, Heini
Mustonen, Jukka
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Tampere Univ Hosp, Dept Internal Med, Tampere 33521, FinlandTampere Univ Hosp, Med Imaging Ctr, Tampere 33521, Finland
机构:
Toho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Suzuki, Aika
Sakamoto, Susumu
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Toho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Sakamoto, Susumu
Kurosaki, Atsuko
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机构:
Fukujuji Hosp, Dept Diagnost Radiol, Tokyo, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Kurosaki, Atsuko
Kurihara, Yasuyuki
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St Lukes Int Hosp, Dept Radiol, Tokyo, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Kurihara, Yasuyuki
Satoh, Keita
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Ikegami Gen Hosp, Div Resp Med, Tokyo, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Satoh, Keita
Usui, Yusuke
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Toho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Usui, Yusuke
Nanki, Toshihiro
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机构:
Toho Univ, Dept Internal Med, Div Rheumatol, Sch Med, Tokyo, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Nanki, Toshihiro
Arimura, Yoshihiro
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机构:
Kyorin Univ, Dept Internal Med 1, Filephrol & Rheumatol, Sch Med, Tokyo, Japan
Kichijoji Asahi Hosp, Tokyo, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Arimura, Yoshihiro
Makino, Hirofumi
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机构:
Okayama Univ, Okayama, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Makino, Hirofumi
Okada, Yasunori
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机构:
Keio Univ, Sch Med, Dept Pathol, Tokyo, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Okada, Yasunori
Harigai, Masayoshi
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机构:
Tokyo Med & Dent Univ, Grad Sch Med & Dent Sci, Dept Pharmacovigilance, Tokyo, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Harigai, Masayoshi
Yamagata, Kunihiro
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机构:
Univ Tsukuba, Fac Med, Dept Nephrol, Ibaraki, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Yamagata, Kunihiro
Sugiyama, Hitoshi
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机构:
Okayama Univ, Dept Human Resource Dev Dialysis Therapy Kidney D, Grad Sch Med Dent & Pharmaceut Sci, Okayama, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Sugiyama, Hitoshi
Dobashi, Hiroaki
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Kagawa Univ, Fac Med, Dept Internal Med, Div Hematol Rheumatol & Resp Med, Takamatsu, Kagawa, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Dobashi, Hiroaki
Ishizu, Akihiro
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机构:
Hokkaido Univ, Fac Hlth Sci, Sapporo, Hokkaido, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
Ishizu, Akihiro
Tsuboi, Naotake
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Nagoya Univ, Grad Sch Med, Internal Med, Dept Nephrol, Nagoya, Aichi, JapanToho Univ, Omori Med Ctr, Dept Resp Med, Ota Ku, Omorinisi 6-11-1, Tokyo 1438541, Japan
机构:
Tzu Chi Univ, Hualien, Taiwan
Buddhist Tzu Hic Gen Hosp, Dept Internal Med, Sect 3, Hualien, TaiwanBuddhist Tzu Hic Gen Hosp, Dept Radiol, Sect 3, Hualien, Taiwan
Lee, Jen-Jyh
Chong, Pau Yuan
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机构:
Buddhist Tzu Hic Gen Hosp, Dept Radiol, Sect 3, Hualien, Taiwan
Tzu Chi Univ, Hualien, TaiwanBuddhist Tzu Hic Gen Hosp, Dept Radiol, Sect 3, Hualien, Taiwan
Chong, Pau Yuan
Lin, Chih-Bin
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机构:
Tzu Chi Univ, Hualien, Taiwan
Buddhist Tzu Hic Gen Hosp, Dept Internal Med, Sect 3, Hualien, TaiwanBuddhist Tzu Hic Gen Hosp, Dept Radiol, Sect 3, Hualien, Taiwan
Lin, Chih-Bin
Hsu, Ai-His
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机构:
Tzu Chi Univ, Hualien, Taiwan
Buddhist Tzu Hic Gen Hosp, Dept Internal Med, Sect 3, Hualien, TaiwanBuddhist Tzu Hic Gen Hosp, Dept Radiol, Sect 3, Hualien, Taiwan
Hsu, Ai-His
Lee, Chuo-Chin
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机构:
Buddhist Tzu Hic Gen Hosp, Dept Radiol, Sect 3, Hualien, Taiwan
Tzu Chi Univ, Hualien, TaiwanBuddhist Tzu Hic Gen Hosp, Dept Radiol, Sect 3, Hualien, Taiwan