Proteus Syndrome High-resolution CT and CT Pulmonary Densitovolumetry Findings

被引：14

作者：

Irion, Klaus L. ^{[1
,2
,3
]}

Hocchegger, Bruno ^{[4
,5
]}

Marchiori, Edson ^{[4
,5
]}

Holemans, John A. ^{[1
,2
,3
]}

Smith, Rupert A. ^{[6
]}

Raja, Ramesh C. ^{[6
]}

Singanayagam, Selvadurai ^{[6
]}

机构：

[1] Liverpool Heart & Chest Hosp NHS Trust, Liverpool, Merseyside, England

[2] Royal Liverpool Univ Hosp, Liverpool, Merseyside, England

[3] Postgrad Program Resp Sci UFRGS, Porto Alegre, RS, Brazil

[4] UFRJ, Postgrad Program Radiol, Rio De Janeiro, Brazil

[5] Univ Fed Fluminense, Niteroi, RJ, Brazil

[6] Pennine Acute Hosp NHS Trust, Great Manchester, Brazil

来源：

JOURNAL OF THORACIC IMAGING | 2009年 / 24卷 / 01期

关键词：

Proteus syndrome; high-resolution computed tomography; chest; quantitative computed tomography; DIAGNOSTIC-CRITERIA; COMPUTED DENSITY; MANIFESTATIONS; MORPHOMETRY; EMPHYSEMA; DEATH;

D O I：

10.1097/RTI.0b013e31818b20cd

中图分类号：

R8 [特种医学]; R445 [影像诊断学];

学科分类号：

1002 ; 100207 ; 1009 ;

摘要：

Cystic transformation of the lungs in Proteus syndrome is considered an important manifestation of this disease. We describe a case of an 11-year-old girl with a diagnosis of Proteus syndrome with lung involvement. Low-dose multidetector computed tomography (CT) revealed extensive diffuse cystic lung disease wit 1 left long predominance. affecting mostly the lower lung zones. The cystic lesions had various sizes and variable wall thickness. Postprocessing using CT histogram densitometric volumetry software (CT densitovolumetry), using the threshold -950 Houndsfield units (HU) for quantifying emphysema, revelled that 31%. of her total lung volume was composed of areas with CT. attenuation values below -950 HU.

引用

页码：45 / 48

页数：4

共 50 条

[1] High-resolution CT findings of pulmonary interstitial glycogenosis
Jason P. Weinman
Christina J. White
Deborah R. Liptzin
Robin R. Deterding
Csaba Galambos
Lorna P. Browne
Pediatric Radiology, 2018, 48 : 1066 - 1072
[2] High-resolution CT findings of pulmonary interstitial glycogenosis
Weinman, Jason P.
White, Christina J.
Liptzin, Deborah R.
Deterding, Robin R.
Galambos, Csaba
Browne, Lorna P.
PEDIATRIC RADIOLOGY, 2018, 48 (08) : 1066 - 1072
[3] High-resolution CT pulmonary findings in children with severe asthma
Bento da Silva, Thiago Krieger
Zanon, Matheus
Altmayer, Stephan
Pacini, Gabriel Sartori
Watte, Guilherme
Stein, Renato
Pitrez, Paulo Marcio
Hochhegger, Bruno
JORNAL DE PEDIATRIA, 2021, 97 (01) : 37 - 43
[4] PULMONARY PARENCHYMAL ABNORMALITIES OF VASCULAR ORIGIN - HIGH-RESOLUTION CT FINDINGS
PRIMACK, SL
MULLER, NL
MAYO, JR
MAYO, JR
REMYJARDIN, M
REMY, J
RADIOGRAPHICS, 1994, 14 (04) : 739 - 746
[5] High-resolution CT pulmonary findings in adults with Gaucher's disease
Yassa, NA
Wilcox, AG
CLINICAL IMAGING, 1998, 22 (05) : 339 - 342
[6] Pulmonary paracoccidioidomycosis and AIDS: High-resolution CT findings in five patients
Marchiori, Edson
Gasparetto, Emerson L.
Escuissato, Dante L.
Souza, Arthur Soares, Jr.
Barreto, Miriam Menna
JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY, 2007, 31 (04) : 605 - 607
[7] High-resolution CT findings of 77 patients with untreated pulmonary paracoccidioidomycosis
Souza, Arthur Soares, Jr.
Gasparetto, Emerson Leandro
Davaus, Taisa
Escuissato, Dante Luiz
Marchiori, Edson
AMERICAN JOURNAL OF ROENTGENOLOGY, 2006, 187 (05) : 1248 - 1252
[8] Silicoproteinosis:: High-resolution CT and histologic findings
Marchiori, E
Ferreira, A
Müller, NL
JOURNAL OF THORACIC IMAGING, 2001, 16 (02) : 127 - 129
[9] Pulmonary lymphangioleiomyomatosis high-resolution CT findings in 11 patients and compared with the literature
Lim, KE
Tsai, YH
Hsu, YL
Hsu, WC
CLINICAL IMAGING, 2004, 28 (01) : 1 - 5
[10] Ketorolac tromethamine associated with diffuse pulmonary haemorrhage: high-resolution CT findings
Rubin, A. Sperb
Hochhegger, B.
Irion, K. L.
Marchiori, E.
Binukrishnan, S. Rajeswari
Moreira, J. S.
Zanetti, G.
BRITISH JOURNAL OF RADIOLOGY, 2010, 83 (991) : E158 - E160

← 1 2 3 4 5 →