Eosinophilic fasciitis and aplastic anemia

被引:0
作者
Falcao, Sandra [1 ,2 ]
Mourao, Ana F. [1 ]
Ribeiro, Celia [1 ]
Pinto, Teresa L. [1 ]
Mateus, Margarida [1 ]
Araujo, Paula [1 ]
Nero, Patricia [1 ]
Pimentao, J. Bravo [1 ]
Branco, J. Cunha [1 ,2 ]
机构
[1] Hosp Egas Moniz, Serv Reumatol, EPE, Ctr Hosp Lisboa Ocidental, P-1349019 Lisbon, Portugal
[2] Univ Nova Lisboa, Fac Ciencias Med, Dept Fisiopatol, P-1200 Lisbon, Portugal
来源
ACTA REUMATOLOGICA PORTUGUESA | 2009年 / 34卷 / 01期
关键词
Eosinophilic Fasciitis; Aplastic Anemia; BONE-MARROW-TRANSPLANTATION; CYCLOSPORINE;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Eosinophilic fasciitis is a rare rheumatic condition characterized by inflammatory thickening of the skin and fascia, peripheral eosinophilia, elevated erythrocyte sedimentation rate and hypergammaglobulinemia. Internal organ involvement is uncommon. It is often difficult to diagnose eosinophilic fasciitis and its course may be variable. Glucocorticoids are most commonly used in the treatment but in many cases they are ineffective, requiring combined immunosuppressive treatment. Several cases of eosinophilic fasciitis and serious, haematological disorders such as immune thrombocytopenia, Hodgkin's disease and aplastic anaemia. have been described. The authors report an atypical severe case of eosinophilic fasciitis complicated by aplastic anaemia. non responsive to treatment.
引用
收藏
页码:120 / 124
页数:5
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