Heart Transplantation in a Patient with Complex Congenital Heart Disease, Physiologic Single Lung, and Severe Pulmonary Hypertension

被引:2
作者
Lee, Hae Won [1 ]
Jung, Jo Won [2 ]
Kim, Ah Young [2 ]
Park, Han Ki [3 ]
机构
[1] Yonsei Univ, Dept Pediat, Coll Med, Seoul, South Korea
[2] Yonsei Univ, Severance Cardiovasc Hosp, Dept Pediat, Coll Med,Div Pediat Cardiol, Seoul, South Korea
[3] Yonsei Univ, Severance Cardiovasc Hosp, Dept Thorac & Cardiovasc Surg, Coll Med,Div Cardiovasc Surg, 50-1 Yonsei Ro, Seoul 03722, South Korea
关键词
Heart defects; congenital; heart transplantation; pulmonary arterial hypertension; physiologic single lung; pediatrics;
D O I
10.3349/ymj.2022.0384
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Here we report a case of successful heart transplantation (HT) in a patient with high risk on HT due to her complex congenital heart disease and its consequent complications; physiologic single lung and severe pulmonary arterial hypertension. HT was suc-cessfully performed in our patient using meticulous perioperative management techniques, such as control of collateral vessels, appropriate donor selection, pulmonary vasodilator therapy, post-transplant extracorporeal membranous oxygenation support, and atrial septostomy for right ventricular unloading.
引用
收藏
页码:1144 / 1146
页数:3
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